Abstract
Children and young adults with potentially lethal cardiac channelopathies often present to medical care with a history of syncope or seizures due to episodic ventricular arrhythmias and associated cerebral hypoperfusion. Catecholaminergic polymorphic ventricular tachycardia is discussed using relevant case example. The pathophysiology and distinguishing clinical features of this condition is reviewed. Cardiac channelopathies can be misdiagnosed as refractory epilepsy when in fact these events represent convulsive syncopes. Knowledge of and suspicion for these arrhythmogenic conditions may improve diagnosis and outcomes.
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© 2015 Springer International Publishing Switzerland
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Cipolletta, L. (2015). Catecholaminergic Polymorphic Ventricular Tachycardia: A Challenging Case of “Epilepsy”. In: Capucci, A. (eds) Clinical Cases in Cardiology. Springer, Cham. https://doi.org/10.1007/978-3-319-19926-9_26
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DOI: https://doi.org/10.1007/978-3-319-19926-9_26
Publisher Name: Springer, Cham
Print ISBN: 978-3-319-19925-2
Online ISBN: 978-3-319-19926-9
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