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Keeling’s Fetal and Neonatal Pathology pp 653–670Cite as

The Reproductive System

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Abstract

A basic requirement of the perinatal autopsy is to document the fetal sex. When this is discordant with the sex documented by the clinical team, it should be communicated rapidly. Occasionally, a disorder of sex development (DSD) may be present, and this should be studied carefully so that the parents may be adequately counseled. Well-documented DSDs, when properly investigated, may also shed new light on our understanding of human reproductive system development. Reproductive tract anomalies can also be associated with complex malformations involving other organs; occasionally a DSD may be the cause of fetal or neonatal demise, such as in cases of pulmonary hypoplasia secondary to hydrometrocolpos.

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Authors and Affiliations

  1. Department of Histopathology, Camelia Botnar Laboratories, Great Ormond Street Hospital for Children, Great Ormond St, London, WC1N 3JH, UK

    William Mifsud MD, PhD

  2. Department of Histopathology, Great Ormond Street Hospital, London, UK

    Liina Kiho MD

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  1. William Mifsud MD, PhD
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  2. Liina Kiho MD
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Correspondence to William Mifsud MD, PhD .

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Editors and Affiliations

  1. Department of Pathology Department of Obstetrics and Gynaecology, University of Adelaide, North Adelaide, South Australia, Australia

    T. Yee Khong

  2. Department of Histopathology, Women’s & Children’s Hospital, North Adelaide, South Australia, Australia

    T. Yee Khong

  3. Department of Histopathology, University Hospitals of Leicester NHS Trust Leicester Royal Infirmary, Leicester, UK

    Roger D. G. Malcomson

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Mifsud, W., Kiho, L. (2015). The Reproductive System. In: Khong, T.Y., Malcomson, R.D.G. (eds) Keeling’s Fetal and Neonatal Pathology. Springer, Cham. https://doi.org/10.1007/978-3-319-19207-9_24

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