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Limb Lengthening and Deformity Correction in Patients with Skeletal Dysplasias

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Pediatric Lower Limb Deformities

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Abstract

Skeletal dysplasias are a group of disorders affecting the growing skeleton. There are many forms of skeletal dysplasia, each with their own unique characteristics. Limb deformities are a common source of morbidity in this population and affect their quality of life and function. Management of these deformities requires a thorough understanding of not only the principles of deformity correction but also the unique challenges that patients with skeletal dysplasia pose for the orthopedic surgeon. Care of these patients requires a multidisciplinary, individualized approach, as many patients have significant extraskeletal comorbidities that need to be appropriately evaluated and managed in addition to correction of their limb deformities.

Limb deformities in this population are often complex, with multifocal and multiplanar deformities being frequent. The unique anatomy in each dysplasia as well as the natural history of these conditions and the complex interplay between deformities and their correction on adjacent joints make deformity correction a formidable task. We outline some of these unique situations, pearls, pitfalls, as well as our approach in correction of lower limb deformities in patients with skeletal dysplasias.

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Authors and Affiliations

  1. Department of orthopedic Surgery, Nemours Alfred I. duPont Hospital for Children, 1600 Rockland Road, Wilmington, DE, 19803, USA

    Mihir M. Thacker MD, Colleen P. Ditro DNP & William Mackenzie

  2. Department of orthopedics, St. Joseph’s Regional Medical Center, 246 Hamburg Turnpike, Suite 305, Wayne, NJ, 07470, USA

    Ellen Dean Davis MD

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  1. Mihir M. Thacker MD
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  3. Colleen P. Ditro DNP
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  4. William Mackenzie
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Correspondence to Mihir M. Thacker MD .

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  1. Professor, Department of Orthopedics; Chief, Division of Pediatric Orthopedics, Rutgers-New Jersey Medical School, Newark, New Jersey, USA

    Sanjeev Sabharwal

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Thacker, M.M., Davis, E.D., Ditro, C.P., Mackenzie, W. (2016). Limb Lengthening and Deformity Correction in Patients with Skeletal Dysplasias. In: Sabharwal, S. (eds) Pediatric Lower Limb Deformities. Springer, Cham. https://doi.org/10.1007/978-3-319-17097-8_19

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