Abstract
This chapter focuses on inclusive features of the nutritional assessment of 2- to 20-year-olds with cystic fibrosis (CF). Multiple components comprise a comprehensive nutrition assessment including obtaining anthropometric and biochemical data; performing a complete clinical assessment; and taking a thorough history of diet, related illnesses, stools, vitamins, minerals, and pancreatic enzyme replacement therapy. Anthropometric data should include weight, height, growth velocity, body mass index (BMI), and may include arm circumference and skinfold measurements. Routine biochemical data should be obtained on a yearly basis and include labs that reflect a basic metabolic profile, plus assessment of liver and vitamin status. The clinical assessment with good physical exam skills should be done at every visit and can provide insight into the nutritional status of the patient with cystic fibrosis. A complete diet history is essential to assess nutrient intake relative to growth indices and provides valuable information regarding intake patterns and practices. Related illnesses including CF liver disease and CF-related diabetes present additional challenges for the patient with CF. A detailed stool and gastrointestinal history is crucial, as this can provide insight into other disease processes which may affect the child’s nutritional status. A thorough vitamin and mineral history assists in ensuring that the patient is receiving proper supplementation in relation to requirements. Finally, a comprehensive pancreatic enzyme replacement therapy history allows for evaluation of adequacy of dosing and updated dosing recommendations. This chapter serves as a general guideline for a basic nutritional assessment.
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Maguiness, K., Bozic, M. (2015). Nutritional Assessment: Age 2–20 Years. In: Yen, E., Leonard, A. (eds) Nutrition in Cystic Fibrosis. Nutrition and Health. Humana Press, Cham. https://doi.org/10.1007/978-3-319-16387-1_7
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DOI: https://doi.org/10.1007/978-3-319-16387-1_7
Publisher Name: Humana Press, Cham
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