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Nutrition and Cystic Fibrosis Related Liver Disease

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Nutrition in Cystic Fibrosis

Part of the book series: Nutrition and Health ((NH))

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Abstract

The liver is commonly affected in cystic fibrosis (CF). While most individuals with CF will have some liver involvement, significant liver disease affects 5–10 % of all CF patients. Despite this, liver disease is the third leading cause of death in CF and accounts for 2.5 % of the overall annual mortality. In this chapter, we will provide an overview of liver involvement in CF, address the disorders that occur in the liver as a result of nutritional deficiencies, and address the nutritional evaluation and management of the two liver diseases in CF that directly affect nutritional status: cholestasis and cirrhosis.

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Authors and Affiliations

  1. Children’s Hospital Colorado, 13123 East 16th Avenue, B290, Aurora, CO, 80045, USA

    Kristin J. Brown M.S., R.D., C.N.S.C., Cathy Lingard R.D. & Michael R. Narkewicz M.D.

  2. Section of Pediatric Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, University of Colorado School of Medicine, Aurora, CO, USA

    Michael R. Narkewicz M.D.

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  1. Kristin J. Brown M.S., R.D., C.N.S.C.
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  2. Cathy Lingard R.D.
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  3. Michael R. Narkewicz M.D.
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Correspondence to Michael R. Narkewicz M.D. .

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Editors and Affiliations

  1. Department of Pediatrics, Division of Gastroenterology, Hepatology and Nutrition, University of California, San Francisco, San Francisco, California, USA

    Elizabeth H. Yen

  2. Gastorenterology and Nutrition, The Johns Hopkins Children’s Center, Baltimore, Maryland, USA

    Amanda Radmer Leonard

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Brown, K.J., Lingard, C., Narkewicz, M.R. (2015). Nutrition and Cystic Fibrosis Related Liver Disease. In: Yen, E., Leonard, A. (eds) Nutrition in Cystic Fibrosis. Nutrition and Health. Humana Press, Cham. https://doi.org/10.1007/978-3-319-16387-1_11

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