Abstract
The eye has many bradytrophic tissues that do not contain blood vessels and have slow metabolism. Similar to other metabolically inert tissues in the body, they are apparently susceptible to pigment deposition. Pigmentation in ochronosis is most apparent on the scleras and cornea, less often in the bulbar conjunctiva, tarsus and eyelid skin. We still cannot explain why ochronotic pigment is not deposited in bradytrophic tissues of the internal eye, parts like corpus vitreum and lens as well. It should be noted that pigment is not deposited in these parts of the eye in other metabolic and endocrine diseases as well.
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Urbánek, T., Rovenský, J. (2015). Manifestations of Alkaptonuric Ochronosis in the Eye. In: Rovenský, J., Urbánek, T., Oľga, B., Gallagher, J. (eds) Alkaptonuria and Ochronosis. Springer, Cham. https://doi.org/10.1007/978-3-319-15108-3_16
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DOI: https://doi.org/10.1007/978-3-319-15108-3_16
Publisher Name: Springer, Cham
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