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Evaluation of the Current Disease Scoring Systems in Familial Mediterranean Fever

  • Chapter
Familial Mediterranean Fever

Part of the book series: Rare Diseases of the Immune System ((RDIS,volume 3))

Abstract

Measurement, as a word, is the assignment of numbers to objects or events. It is a cornerstone for technology, economics, and social sciences and must be part a of the medical discipline as well. Lord Kelvin emphasized 13 decades ago (in 1883): “When you can measure what you are speaking about and express it in numbers, you know something about it” [1]. It is also essential that measurements are as accurate as possible and include all that account. However, health is a multidimensional, subjective, and qualitatively natured concept that is usually expressed in terms of presence or absence of life-threatening illness (damage, physical disability), risk factors for mortality, activity and severity of disease, and overall health-related performance (satisfactory social functioning and emotional well-being). Thus, an accurate measurement of health status is a real challenge currently achieved only by a combination of multiple scoring tools.

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Author information

Authors and Affiliations

  1. Division of Pediatric Rheumatology, FMF Arthritis Vasculitis and Orphan Disease Research Center (FAVOR), Gulhane Military, Medical Faculty, Etlik/Ankara, 06018, Turkey

    Erkan Demirkaya MD, MSc

  2. Department of Medicine F, Sheba Medical Center, Tel-Hashomer, Israel

    Avi Livneh

  3. Heller Institute of Medical Research, Sheba Medical Center, Tel-Hashomer, Israel

    Avi Livneh

  4. Rheumatology Unit, Sheba Medical Center, Tel-Hashomer, Israel

    Avi Livneh

  5. The Sackler School of Medicine, Tel Aviv University, Tel Aviv, Israel

    Avi Livneh

Authors
  1. Erkan Demirkaya MD, MSc
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  2. Avi Livneh
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Corresponding author

Correspondence to Erkan Demirkaya MD, MSc .

Editor information

Editors and Affiliations

  1. II Paediatric Unit-Rheumatology, G. Gaslini Institute, Genova, Genova, Italy

    Marco Gattorno

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Demirkaya, E., Livneh, A. (2015). Evaluation of the Current Disease Scoring Systems in Familial Mediterranean Fever. In: Gattorno, M. (eds) Familial Mediterranean Fever. Rare Diseases of the Immune System, vol 3. Springer, Cham. https://doi.org/10.1007/978-3-319-14615-7_7

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  • DOI: https://doi.org/10.1007/978-3-319-14615-7_7

  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-14614-0

  • Online ISBN: 978-3-319-14615-7

  • eBook Packages: MedicineMedicine (R0)

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