Abstract
Definition: Highly malignant poorly differentiated tumors composed by small round cells. The current definition includes the historical entities of Ewing sarcoma, peripheral primitive neuroectodermal tumor, and Askin tumor, all of which share the same oncogenic fusions and similar biologic behavior. Some present cytologic neurogenic features (PNET): otherwise, they do not differ from ES, and therefore they are considered as a unique entity.
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Fabbri, N., Manfrini, M. (2014). Ewing Sarcoma (ES). In: Picci, P., Manfrini, M., Fabbri, N., Gambarotti, M., Vanel, D. (eds) Atlas of Musculoskeletal Tumors and Tumorlike Lesions. Springer, Cham. https://doi.org/10.1007/978-3-319-01748-8_47
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DOI: https://doi.org/10.1007/978-3-319-01748-8_47
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