Summary
Epidemiological data of the Italian CF population followed at Regional Health Care Centres are available from the Italian National Cystic Fibrosis Register. Data updated at 31.12.1994 are presented. It is important to note that over 29% of patients are older than 18 years, the cumulative survival probability being equal to 0.58 at 25 years. Both structures for the care of Italian CF patients (16 Regional CF Centres and CF support services) and the new laws passed in 1993 to facilitate care for CF patients are presented. Prevalence of P. aeruginosa and B. cepacia are shown together with various aspects of prevention of viral infections, and of Pseudomonal cross-infection. Therapy strategies against lung infection (early colonization, chronic infection; criteria for inhospital or home therapy) adopted in the different Italian centres are also presented. Prognosis and quality of life of Italian CF patients are improving thanks to this global approach to the disease.
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© 1996 Birkhäuser Verlag Basel/Switzerland
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Padoan, R., Pianaroli, A., Giunta, A. (1996). The General Approach to Cystic Fibrosis Pulmonary Infection in Italy. In: Bauernfeind, A., Marks, M.I., Strandvik, B. (eds) Cystic Fibrosis Pulmonary Infections: Lessons from Around the World. Respiratory Pharmacology and Pharmacotherapy. Birkhäuser Basel. https://doi.org/10.1007/978-3-0348-7359-8_17
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DOI: https://doi.org/10.1007/978-3-0348-7359-8_17
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