Skip to main content

Surgical Problems of Children with Physical Disabilities

  • Chapter
  • First Online:
Pediatric Surgery
  • 95 Accesses

Abstract

Children with physical disabilities and children with special health care needs (CSHCN) benefit from a cooperative relationship between parents, medical providers, and pediatric surgeons in managing their surgical needs. This benefit is manifested by simplification of the care provided to children by parents, in order to improve quality of life, development of trust and relationships between parents and caregivers to guide thoughtful decisions about surgical interventions, forging an understanding of the complexities of surgical care by all concerned, and the selection of appropriate surgical candidates and expeditious evaluation of perioperative problems. This chapter focuses on the general principles of family-centered care and common perioperative considerations for CSHCN patients and serves to educate the pediatric surgeon about the importance of comprehensive care and special considerations for children with common conditions that encompass the patient with a physical disability. Pediatric surgical CSHCN patients typically have either a genetic malformation syndrome (i.e., Trisomy 21), cerebral palsy or neurologic impairment, complex congenital heart disease, or a spectrum of comorbid conditions as the result of a congenital malformation. Albeit by no means exhaustive, this chapter will serve to highlight some of the common challenges that must be addressed by the pediatric surgeon caring for this complex group of patients.

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

Chapter
USD 29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD 149.00
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD 199.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info
Hardcover Book
USD 279.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

Similar content being viewed by others

References

  • Administration MaCHBotHRaS. National Survey of Children with Special Health Care Needs 2016. Available from: https://www.cdc.gov/nchs/slaits/cshcn.htm#anchor_1551498339279

  • Adzick NS, Thom EA, Spong CY, Brock JW 3rd, Burrows PK, Johnson MP et al (2011) A randomized trial of prenatal versus postnatal repair of myelomeningocele. N Engl J Med 364(11):993–1004

    CAS  PubMed  PubMed Central  Google Scholar 

  • Albavera-Hernández C, Rodríguez JM, Idrovo AJ (2009) Safety of botulinum toxin type A among children with spasticity secondary to cerebral palsy: a systematic review of randomized clinical trials. Clin Rehabil 23(5):394–407

    PubMed  Google Scholar 

  • Al-Jazairi AS, Al-Suhaibani LK, Al-Mehizia RA, Al-Khani S, Lewis G, De Vol EB et al (2017) Impact of a medication reconciliation program on cardiac surgery patients. Asian Cardiovasc Thorac Ann 25(9):579–585

    PubMed  Google Scholar 

  • Allen J, Molloy E, McDonald D (2019) Severe neurological impairment: a review of the definition. Dev Med Child Neurol

    Google Scholar 

  • Antonelli RC, Stille CJ, Antonelli DM (2008) Care coordination for children and youth with special health care needs: a descriptive, multisite study of activities, personnel costs, and outcomes. Pediatrics 122(1):e209-16

    PubMed  Google Scholar 

  • Berry JG, Hall M, Cohen E, O'Neill M, Feudtner C (2015) Ways to identify children with medical complexity and the importance of why. J Pediatr 167(2):229–237

    PubMed  PubMed Central  Google Scholar 

  • Brooks J, Day S, Shavelle R, Strauss D (2011) Low weight, morbidity, and mortality in children with cerebral palsy: new clinical growth charts. Pediatrics 128(2):e299–e307

    PubMed  Google Scholar 

  • Brown ML, Dinardo JA, Nasr VG (2020) Anesthesia in pediatric patients with congenital heart disease undergoing noncardiac surgery: defining the risk. J Cardiothorac Vasc Anesth 34(2):470–478

    PubMed  Google Scholar 

  • Cloake T, Gardner A (2016) The management of scoliosis in children with cerebral palsy: a review. J Spine Surg 2(4):299–309

    PubMed  PubMed Central  Google Scholar 

  • Costa A, Richman DC (2016) Implantable devices: assessment and perioperative management. Anesthesiol Clin 34(1):185–199

    PubMed  Google Scholar 

  • De Queiroz M, Combet S, Bérard J, Pouyau A, Genest H, Mouriquand P et al (2009) Latex allergy in children: modalities and prevention. Paediatr Anaesth 19(4):313–319

    PubMed  Google Scholar 

  • van Dyck PC, McPherson M, Strickland BB, Nesseler K, Blumberg SJ, Cynamon ML et al (2002) The national survey of children with special health care needs. Ambul Pediatr 2(1):29–37

    PubMed  Google Scholar 

  • Fallat ME, Deshpande JK (2004) Do-not-resuscitate orders for pediatric patients who require anesthesia and surgery. Pediatrics 114(6):1686–1692

    PubMed  Google Scholar 

  • Ferland CE, Vega E, Ingelmo PM (2018) Acute pain management in children: challenges and recent improvements. Curr Opin Anaesthesiol 31(3):327–332

    PubMed  Google Scholar 

  • Fraser JD, Aguayo P, Sharp SW, Holcomb IG, Ostlie DJ, St Peter SD (2009) The safety of laparoscopy in pediatric patients with ventriculoperitoneal shunts. J Laparoendosc Adv Surg Tech A 19(5):675–678

    PubMed  Google Scholar 

  • Freundlich K (2017) Pressure injuries in medically complex children: a review. Children (Basel) 4(4)

    Google Scholar 

  • Friedrichsdorf SJ (2017) Multimodal pediatric pain management (part 2). Pain Manage 7(3):161–166

    Google Scholar 

  • Giglia TM, Massicotte MP, Tweddell JS, Barst RJ, Bauman M, Erickson CC et al (2013) Prevention and treatment of thrombosis in pediatric and congenital heart disease: a scientific statement from the American Heart Association. Circulation 128(24):2622–2703

    PubMed  Google Scholar 

  • Goldberg H, Aharony S, Levy Y, Sivan B, Baniel J, Ben MD (2016) Low prevalence of latex allergy in children with spinal dysraphism in non-latex-free environment. J Pediatr Urol 12(1):52.e1–5

    PubMed  Google Scholar 

  • Goldson E, Louch G, Washington K, Scheu H (2006) Guidelines for the care of the child with special health care needs. Adv Pediatr 53(1):165–182

    PubMed  Google Scholar 

  • Horace A, Ahmed F (2015) Polypharmacy in pediatric patients and opportunities for pharmacists’ involvement. Integr Pharm Res Pract 4:113

    PubMed  PubMed Central  Google Scholar 

  • Howell HB, Zaccario M, Kazmi SH, Desai P, Sklamberg FE, Mally P (2019) Neurodevelopmental outcomes of children with congenital heart disease: a review. Curr Probl Pediatr Adolesc Health Care 49(10):100685

    PubMed  Google Scholar 

  • Jacobs ML, O'Brien SM, Jacobs JP, Mavroudis C, Lacour-Gayet F, Pasquali SK et al (2013) An empirically based tool for analyzing morbidity associated with operations for congenital heart disease. J Thorac Cardiovasc Surg 145(4):1046–57.e1

    PubMed  Google Scholar 

  • Janik JS, Burrington JD, Janik JE, Wayne ER, Chang JH, Rothenberg SS (1997) Anterior exposure of spinal deformities and tumors: a 20-year experience. J Pediatr Surg 32(6):852–859

    CAS  PubMed  Google Scholar 

  • Janvier A, Farlow B, Barrington K (2016) Cardiac surgery for children with trisomies 13 and 18: Where are we now?

    Google Scholar 

  • Jones L, Bellis MA, Wood S, Hughes K, McCoy E, Eckley L et al (2012) Prevalence and risk of violence against children with disabilities: a systematic review and meta-analysis of observational studies. Lancet 380(9845):899–907

    PubMed  Google Scholar 

  • Kuo DZ, Berry JG, Glader L, Morin MJ, Johaningsmeir S, Gordon J (2016) Health services and health care needs fulfilled by structured clinical programs for children with medical complexity. J Pediatr 169:291-6.e1

    PubMed  Google Scholar 

  • Lake W, Shah H (2019) Intrathecal Baclofen infusion for the treatment of movement disorders. Neurosurg Clin N Am 30(2):203–209

    PubMed  Google Scholar 

  • Lam DJ, Lee JZ, Chua JH, Lee YT, Lim KB (2014) Superior mesenteric artery syndrome following surgery for adolescent idiopathic scoliosis: a case series, review of the literature, and an algorithm for management. J Pediatr Orthop B 23(4):312–318

    PubMed  Google Scholar 

  • Lauriti G, Lisi G, Lelli Chiesa P, Zani A, Pierro A (2018) Gastroesophageal reflux in children with neurological impairment: a systematic review and meta-analysis. Pediatr Surg Int 34(11):1139–1149

    PubMed  Google Scholar 

  • Lerner CF, Klitzner TS (2017) The medical home at 50: are children with medical complexity the key to proving its value? Acad Pediatr

    Google Scholar 

  • Lindberg T (1999) The child’s right to health and treatment. Med Confl Surviv 15(4):336–341

    CAS  PubMed  Google Scholar 

  • Malone PS, Ransley PG, Kiely EM (1990) Preliminary report: the antegrade continence enema. Lancet 336(8725):1217–1218

    CAS  PubMed  Google Scholar 

  • Marpole R, Blackmore AM, Gibson N, Cooper MS, Langdon K, Wilson AC (2020) Evaluation and management of respiratory illness in children with cerebral palsy. Front Pediatr 8:333

    PubMed  PubMed Central  Google Scholar 

  • Morrison PJ, Spence R (2005) Genetics for surgeons. Remedica, London

    Google Scholar 

  • Naftel RP, Argo JL, Shannon CN, Taylor TH, Tubbs RS, Clements RH et al (2011) Laparoscopic versus open insertion of the peritoneal catheter in ventriculoperitoneal shunt placement: review of 810 consecutive cases. J Neurosurg 115(1):151–158

    PubMed  Google Scholar 

  • Neff JM, Clifton H, Popalisky J, Zhou C (2015) Stratification of children by medical complexity 15(2):191–196

    Google Scholar 

  • Norton RP, Patel D, Kurd MF, Picetti GD, Vaccaro AR (2007) The use of thoracoscopy in the management of adolescent idiopathic scoliosis. Spine 32(24):2777–2785

    PubMed  Google Scholar 

  • Nowak CB (2015) Recognition and prevention of child abuse in the child with disability. Am J Med Genet C Semin Med Genet 169(4):293–301

    PubMed  Google Scholar 

  • Okun A (2010) Ethics for the pediatrician: children who have special health-care needs: ethical issues. Pediatr Rev 31(12):514–517

    PubMed  Google Scholar 

  • Perkins J, Agrawal R (2018) Protecting rights of children with medical complexity in an era of spending reduction. Pediatrics 141(Suppl 3):S242–S2S9

    PubMed  Google Scholar 

  • Petska HW, Gordon JB, Jablonski D, Sheets LK (2017) The intersection of medical child abuse and medical complexity. Pediatr Clin N Am 64(1):253–264

    Google Scholar 

  • Pordes E, Gordon J, Sanders LM, Cohen E (2018) Models of care delivery for children with medical complexity. Pediatrics 141(Supplement 3):S212–SS23

    PubMed  Google Scholar 

  • Russell CJ, Simon TD (2014) Care of children with medical complexity in the hospital setting. Pediatr Ann 43(7):e157–ee62

    PubMed  Google Scholar 

  • Schor EL (2003) Family pediatrics: report of the Task Force on the Family. Pediatrics 111(6 Pt 2):1541–1571

    PubMed  Google Scholar 

  • Stille CJ, Antonelli RC (2004) Coordination of care for children with special health care needs. Curr Opin Pediatr 16(6):700–705

    PubMed  Google Scholar 

  • Stone JJ, Walker CT, Jacobson M, Phillips V, Silberstein HJ (2013) Revision rate of pediatric ventriculoperitoneal shunts after 15 years. J Neurosurg Pediatr 11(1):15–19

    PubMed  Google Scholar 

  • Sulkowski JP, Cooper JN, McConnell PI, Pasquali SK, Shah SS, Minneci PC et al (2014) Variability in noncardiac surgical procedures in children with congenital heart disease. J Pediatr Surg 49(11):1564–1569

    PubMed  PubMed Central  Google Scholar 

  • Sullivan PM, Knutson JF (2000) Maltreatment and disabilities: a population-based epidemiological study. Child Abuse Negl 24(10):1257–1273

    CAS  PubMed  Google Scholar 

  • Sullivan N, Schoelles KM (2013) Preventing in-facility pressure ulcers as a patient safety strategy: a systematic review. Ann Intern Med 158(5 Pt 2):410–416

    PubMed  Google Scholar 

  • Tobias JD (2018) Preoperative anesthesia evaluation. Semin Pediatr Surg 27(2):67–74

    PubMed  Google Scholar 

  • Tomoum HY, Badawy NB, Hassan NE, Alian KM (2010) Anthropometry and body composition analysis in children with cerebral palsy. Clin Nutr 29(4):477–481

    PubMed  Google Scholar 

  • Velde M, Novak T, Badawi. (2019) Early diagnosis and classification of cerebral palsy: an historical perspective and barriers to an early diagnosis. J Clin Med 8(10):1599

    Google Scholar 

  • Visscher M, King A, Nie AM, Schaffer P, Taylor T, Pruitt D et al (2013) A quality-improvement collaborative project to reduce pressure ulcers in PICUs. Pediatrics 131(6):e1950–e1960

    PubMed  PubMed Central  Google Scholar 

  • Warnes CA, Williams RG, Bashore TM, Child JS, Connolly HM, Dearani JA et al (2008) ACC/AHA 2008 guidelines for the management of adults with congenital heart disease: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (Writing Committee to Develop Guidelines on the Management of Adults with Congenital Heart Disease). Developed in Collaboration with the American Society of Echocardiography, Heart Rhythm Society, International Society for Adult Congenital Heart Disease, Society for Cardiovascular Angiography and Interventions, and Society of Thoracic Surgeons. J Am Coll Cardiol 52(23):e143–e263

    PubMed  Google Scholar 

  • Watkins SC, McNew BS, Donahue BS (2013) Risks of noncardiac operations and other procedures in children with complex congenital heart disease. Ann Thorac Surg 95(1):204–211

    PubMed  Google Scholar 

  • Weiss MA, Marchese S, Zhang L (2019) Effective care management for children with special health care needs in the era of value-based payment. Clin Pediatr 58(9):949–956

    Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Corresponding author

Correspondence to Casey M. Calkins .

Editor information

Editors and Affiliations

Rights and permissions

Reprints and permissions

Copyright information

© 2023 Springer Nature Switzerland AG

About this chapter

Check for updates. Verify currency and authenticity via CrossMark

Cite this chapter

Calkins, C.M. (2023). Surgical Problems of Children with Physical Disabilities. In: Puri, P., Höllwarth, M.E. (eds) Pediatric Surgery. Springer, Cham. https://doi.org/10.1007/978-3-030-81488-5_16

Download citation

  • DOI: https://doi.org/10.1007/978-3-030-81488-5_16

  • Published:

  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-81487-8

  • Online ISBN: 978-3-030-81488-5

  • eBook Packages: MedicineMedicine (R0)

Publish with us

Policies and ethics