Abstract
Although many aspects of Chiari malformation type I (CM I) natural history remain unsolved, some progress is being made. Recently, several groups have reported on CM I natural history in selected groups of patients that were managed without surgery. Each of these studies followed patients for several years. In general, the natural history for this subgroup of Chiari patients is benign, although cases of clinical progression as well as spontaneous improvement were seen. The available data clarify the natural history of CM I for the subgroup of CM I patients that are considered to be asymptomatic or minimally symptomatic and without neurological deficits. Spinal syringes in patients with CM I follow a varied and unpredictable natural course.
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The author would like to thank Holly Wagner for providing editorial assistance.
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Maher, C.O. (2020). Natural History of Chiari Malformations. In: Tubbs, R., Turgut, M., Oakes, W. (eds) The Chiari Malformations. Springer, Cham. https://doi.org/10.1007/978-3-030-44862-2_22
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