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Chiari I Malformation and Craniosynostosis

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The Chiari Malformations

Abstract

Hindbrain hernia is often seen in various craniosynostoses. Although these can be seen in single-suture craniosynostosis, syndromic craniosynostosis has a greater risk of having Chiari malformation type I (CM I). In particular, patients with Apert and Crouzon syndromes should be investigated for CM I. Today, simultaneous or consecutive cranial vault remodeling and suboccipital decompression are standard treatments in these complex patients with combined craniosynostosis and CM I, but further studies are needed because of the complexity of surgical care.

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Authors and Affiliations

  1. Department of Neurosurgery, Aydın Adnan Menderes University School of Medicine, Efeler, Aydın, Turkey

    Mehmet Turgut

  2. Department of Neurosurgery, Tulane University School of Medicine, New Orleans, LA, USA

    R. Shane Tubbs

  3. Department of Neurosurgery and Ochsner Neuroscience Institute, Ochsner Health System, New Orleans, LA, USA

    R. Shane Tubbs

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  1. Mehmet Turgut
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Editors and Affiliations

  1. Department of Neurosurgery, Tulane University School of Medicine, New Orleans, LA, USA

    R. Shane Tubbs

  2. Department of Neurosurgery, Aydın Adnan Menderes University School of Medicine, Efeler, Aydın, Turkey

    Mehmet Turgut

  3. Departments of Neurosurgery and Pediatrics, University of Alabama, Birmingham, AL, USA

    W. Jerry Oakes

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Turgut, M., Tubbs, R.S. (2020). Chiari I Malformation and Craniosynostosis. In: Tubbs, R., Turgut, M., Oakes, W. (eds) The Chiari Malformations. Springer, Cham. https://doi.org/10.1007/978-3-030-44862-2_20

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