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Understanding Treatment Adherence in Cystic Fibrosis: Challenges and Opportunities

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Cystic Fibrosis

Part of the book series: Respiratory Medicine ((RM))

Abstract

Significant advancements in the treatment of cystic fibrosis (CF) have led to drastically improved medical outcomes for those living with this illness. While these improvements have increased life expectancy and resulted in better quality of life, managing the daily care required to stay healthy is burdensome and complex. A time-intensive daily CF treatment regimen may be difficult to maintain and can interfere with many aspects of one’s life. Many factors impact how well an individual adheres to recommendations of their healthcare team. Understanding the barriers and facilitators of treatment adherence in CF is critical as well as the interventions available to help those with this disease live better lives while managing their health.

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Authors and Affiliations

  1. University of Colorado School of Medicine, Children’s Hospital Colorado, Department of Psychiatry, Aurora, CO, USA

    Emily F. Muther

  2. Michigan Medicine C.S. Mott Children’s Hospital, Department of Pediatrics, Ann Arbor, MI, USA

    Jennifer L. Butcher

  3. Johns Hopkins School of Medicine, Department of Medicine, Baltimore, MD, USA

    Kristin A. Riekert

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  1. Emily F. Muther
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  2. Jennifer L. Butcher
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  3. Kristin A. Riekert
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Correspondence to Emily F. Muther .

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Editors and Affiliations

  1. The University of North Carolina at Chapel Hill, Department of Pediatrics, UNC Children’s Hospital, Chapel Hill, NC, USA

    Stephanie Duggins Davis

  2. Department of Pediatrics, University of Washington School of Medicine, Division of Pulmonary and Sleep Medicine, Seattle Children’s Hospital, Seattle, WA, USA

    Margaret Rosenfeld

  3. Department of Pediatrics, Indiana University School of Medicine, Division of Pediatric Pulmonology, Allergy and Sleep Medicine, Riley Hospital for Children at IU Health, Indianapolis, IN, USA

    James Chmiel

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Muther, E.F., Butcher, J.L., Riekert, K.A. (2020). Understanding Treatment Adherence in Cystic Fibrosis: Challenges and Opportunities. In: Davis, S., Rosenfeld, M., Chmiel, J. (eds) Cystic Fibrosis. Respiratory Medicine. Humana, Cham. https://doi.org/10.1007/978-3-030-42382-7_22

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