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Tumors of the Fetus and Infant

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Fetal and Neonatal Eye Pathology

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Abstract

Congenital tumors, in particular orbital teratomas, develop in the fetus and may be recognized prenatally during ultrasound examinations or within the first few years after birth. Retinoblastoma is the most frequent intraocular malignant tumor in children. Extremely rare in fetal eyes, it may develop soon after birth and in most cases is recognized within the first 3 years of life, owing to leukocoria or screening of children with a positive family history. Medulloepithelioma of the eye is a rare tumor of the ciliary body that usually presents after 2 years of age, but it can be seen in newborns or adults.

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Author information

Authors and Affiliations

  1. Department of Pathology, Section Ophthalmic Pathology, Erasmus MC University Medical Center Rotterdam, Rotterdam, The Netherlands

    Robert M. Verdijk

  2. Department of Pathology, Leiden University Medical Center, Leiden, The Netherlands

    Robert M. Verdijk

  3. Department of Ophthalmology, University Hospital Bonn, Bonn, Germany

    Martina C. Herwig-Carl

Authors
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  2. Martina C. Herwig-Carl
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Correspondence to Robert M. Verdijk .

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Verdijk, R.M., Herwig-Carl, M.C. (2020). Tumors of the Fetus and Infant. In: Fetal and Neonatal Eye Pathology. Springer, Cham. https://doi.org/10.1007/978-3-030-36079-5_8

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  • DOI: https://doi.org/10.1007/978-3-030-36079-5_8

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-36078-8

  • Online ISBN: 978-3-030-36079-5

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