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Diagnosis of Musculoskeletal Tumors and Tumor-like Conditions pp 223–231Cite as

Small Blue Round Cell Tumors

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Abstract

Definition: High-grade malignant poorly differentiated tumor composed of small round cells. The current definition includes several historical entities, such as Ewing sarcoma, peripheral primitive neuroectodermal tumor (PNET), Askin’s tumor (Ewing sarcoma of the chest wall), and adamantinoma-like Ewing sarcoma, all of which share the same oncogenic fusions and similar biologic behavior, and therefore are currently considered as a unique entity defined as Ewing sarcoma family of tumors (EFTs).

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Author information

Authors and Affiliations

  1. Orthopedic Oncology Department, IRCCS Istituto Ortopedico Rizzoli, Bologna, Italy

    Marco Manfrini

  2. Department of Pathology, IRCCS Istituto Ortopedico Rizzoli, Bologna, Italy

    Marco Gambarotti

Authors
  1. Marco Manfrini
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  2. Marco Gambarotti
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Corresponding author

Correspondence to Marco Manfrini .

Editor information

Editors and Affiliations

  1. I.S.G. Italian Sarcoma Group, Bologna, Italy

    Piero Picci

  2. IIIrd Clinic of Orthopaedic Oncology, Istituto Ortopedico Rizzoli, Bologna, Italy

    Marco Manfrini

  3. Istituto Ortopedico Rizzoli, Bologna, Italy

    Davide Maria Donati

  4. Department of Pathology, IRCCS Istituto Ortopedico Rizzoli, Bologna, Italy

    Marco Gambarotti

  5. Department of Pathology, IRCCS Istituto Ortopedico Rizzoli, Bologna, Italy

    Alberto Righi

  6. Istituto Rizzoli, Bologna, Italy

    Daniel Vanel

  7. Department of Medicine, University of Padua School of Medicine, Padua, Italy

    Angelo Paolo Dei Tos

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Manfrini, M., Gambarotti, M. (2020). Small Blue Round Cell Tumors. In: Picci, P., et al. Diagnosis of Musculoskeletal Tumors and Tumor-like Conditions. Springer, Cham. https://doi.org/10.1007/978-3-030-29676-6_39

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  • DOI: https://doi.org/10.1007/978-3-030-29676-6_39

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-29675-9

  • Online ISBN: 978-3-030-29676-6

  • eBook Packages: MedicineMedicine (R0)

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