Skip to main content

Osteofibrous Dysplasia of Long Bones

  • Chapter
  • First Online:
Diagnosis of Musculoskeletal Tumors and Tumor-like Conditions
  • 1181 Accesses

Abstract

Definition: Benign fibro-osseous lesion of bone, characteristically involving cortical bone of the anterior mid-shaft of the tibia of young patients. This lesion is also called osteofibrous dysplasia of long bones (DOFOL), Kempson-Campanacci disease, and ossifying fibroma of long bones.

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

eBook
USD 16.99
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD 109.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info
Hardcover Book
USD 159.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

Selected Bibliography

  • Benassi MS, Campanacci L, Gamberi G, Ferrari C, Picci P, Sangiorgi L, Campanacci M. Cytokeratin expression and distribution in adamantinoma of the long bones and osteofibrous dysplasia of tibia and fibula. An immunohistochemical study correlated to histogenesis. Histopathology. 1994;25(1):71–6.

    Article  CAS  Google Scholar 

  • Bethapudi S, Ritchie DA, Macduff E, Straiton J. Imaging in osteofibrous dysplasia, osteofibrous dysplasia-like adamantinoma, and classic adamantinoma. Clin Radiol. 2014;69(2):200–8.

    Article  CAS  Google Scholar 

  • Campanacci M, Laus M. Osteofibrous dysplasia of the tibia and fibula. J Bone Joint Surg Am. 1981;63(3):367–75.

    Article  CAS  Google Scholar 

  • Gleason BC, Liegl-Atzwanger B, Kozakewich HP, Connolly S, Gebhardt MC, Fletcher JA, Perez-Atayde AR. Osteofibrous dysplasia and adamantinoma in children and adolescents: a clinicopathologic reappraisal. Am J Surg Pathol. 2008;32(3):363–76.

    Article  Google Scholar 

  • Khanna M, Delaney D, Tirabosco R, Saifuddin A. Osteofibrous dysplasia, osteofibrous dysplasia-like adamantinoma and adamantinoma: correlation of radiological imaging features with surgical histology and assessment of the use of radiology in contributing to needle biopsy diagnosis. Skeletal Radiol. 2008;37(12):1077–84.

    Article  Google Scholar 

  • Most MJ, Sim FH, Inwards CY. Osteofibrous dysplasia and adamantinoma. J Am Acad Orthop Surg. 2010;18(6):358–66.

    Article  Google Scholar 

  • Puchner SE, Varga R, Hobusch GM, Kasparek M, Panotopoulos J, Lang S, Windhager R, Funovics PT. Long-term outcome following treatment of adamantinoma and osteofibrous dysplasia of long bones. Orthop Traumatol Surg Res. 2016;102(7):925–32.

    Article  CAS  Google Scholar 

  • Simoni P, Scarciolla L, Mutijima E, Zobel BB. Osteofibrous dysplasia: a case report and review of the literature. Radiol Case Rep. 2015;6(4):546.

    Article  Google Scholar 

  • Taylor RM, Kashima TG, Ferguson DJ, Szuhai K, Hogendoorn PC, Athanasou NA. Analysis of stromal cells in osteofibrous dysplasia and adamantinoma of long bones. Mod Pathol. 2012;25:56–64.

    Article  CAS  Google Scholar 

  • Vigorita VJ, Hogendoorn PCW, Sawyer JR. Osteofibrous dysplasia. World Health Organization classification of tumours. Pathology and genetics of tumours of soft tissue and bone. Lyon: IARC Press; 2013. p. 354–5.

    Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Corresponding author

Correspondence to Alberto Righi .

Editor information

Editors and Affiliations

Rights and permissions

Reprints and permissions

Copyright information

© 2020 Springer Nature Switzerland AG

About this chapter

Check for updates. Verify currency and authenticity via CrossMark

Cite this chapter

Righi, A. (2020). Osteofibrous Dysplasia of Long Bones. In: Picci, P., et al. Diagnosis of Musculoskeletal Tumors and Tumor-like Conditions. Springer, Cham. https://doi.org/10.1007/978-3-030-29676-6_13

Download citation

  • DOI: https://doi.org/10.1007/978-3-030-29676-6_13

  • Published:

  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-29675-9

  • Online ISBN: 978-3-030-29676-6

  • eBook Packages: MedicineMedicine (R0)

Publish with us

Policies and ethics