Abstract
Vasculitic neuropathy is a rare debilitating but treatable peripheral neuropathy. The classic manifestation is a mononeuropathy multiplex pattern of sensorimotor disturbances, but it can also present as a symmetric length-dependent polyneuropathy. Nerve and muscle biopsies are important in the diagnostic workup, with the combination increasing the diagnostic yield. Specific pathologic findings include fibrinoid necrosis and transmural inflammation. Long-term combined immunosuppressive therapy is often required. We present a case of a woman who presented with a subacute onset of progressive painful sensory and motor disturbances without systemic manifestations. Laboratory and pathological findings were confirmatory for a lupus-associated vasculitic neuropathy.
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Khan, S., Cai, C. (2020). A 59-Year-Old Woman with Subacute Lower Limb Weakness and Painful Paresthesia. In: Zhou, L., Burns, D., Cai, C. (eds) A Case-Based Guide to Neuromuscular Pathology. Springer, Cham. https://doi.org/10.1007/978-3-030-25682-1_32
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DOI: https://doi.org/10.1007/978-3-030-25682-1_32
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