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Pulmonary Venous Drainage Disorders

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Imaging in Pediatric Pulmonology

Abstract

Congenital pulmonary venous drainage disorders, which arise from abnormal embryonic venous development, occur in a diverse spectrum in the pediatric population. Although echocardiography with pulsed Doppler remains the initial investigation of choice in the evaluation of pulmonary venous developmental anomalies particularly in infants and young children, noninvasive imaging studies such as multidetector computed tomography and magnetic resonance imaging have established a prominent role in the initial diagnosis and further characterization of this group of disorders. In this chapter, we review (1) embryology, (2) epidemiology, (3) anatomy, (4) clinical presentation, (5) preoperative imaging evaluation, (6) management, and (7) postoperative imaging evaluation of congenital pulmonary venous drainage disorders in the pediatric population.

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Authors and Affiliations

  1. Department of Radiology, Boston Children’s Hospital and Harvard Medical School, Boston, MA, USA

    Edward Y. Lee & Sanjay P. Prabhu

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  1. Edward Y. Lee
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  2. Sanjay P. Prabhu
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Correspondence to Edward Y. Lee .

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Editors and Affiliations

  1. Department of Radiology, Harvard Medical School Boston Children’s Hospital, Boston, MA, USA

    Robert H. Cleveland

  2. Department of Radiology, Harvard Medical School Boston Children’s Hospital, Boston, MA, USA

    Edward Y. Lee

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Lee, E.Y., Prabhu, S.P. (2020). Pulmonary Venous Drainage Disorders. In: Cleveland, R., Lee, E. (eds) Imaging in Pediatric Pulmonology. Springer, Cham. https://doi.org/10.1007/978-3-030-23979-4_13

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  • DOI: https://doi.org/10.1007/978-3-030-23979-4_13

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  • Online ISBN: 978-3-030-23979-4

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