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Critical Care of Children with Heart Disease pp 393–404Cite as

Double Outlet Right Ventricle

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Abstract

Double outlet right ventricle is a type of anomalous ventriculoarterial connection that represents 0.5–1.5% of congenital cardiac defects and can express several “phenotypes.” This conotruncal anomaly presents with a wide spectrum of anatomical forms depending on the location of the ventricular septal defect, the relationship between the great vessels and the ventricular cavities, and the presence of a pulmonary flow obstruction. Furthermore, DORV may or may not be associated with hypoplasia of one ventricle. This chapter provides an overview of the facets related to diagnosis and medical and surgical management of this cardiac malformation.

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Author information

Authors and Affiliations

  1. Department of Pediatrics, Children’s Hospital of Richmond, Virginia Commonwealth University, Richmond, VA, USA

    Uyen Truong

  2. Associate Medical Director, CHCO Heart Institute, Head, Pediatric Cardiac Critical Care Program & Inpatient Services, Director, Cardiac Intensive Care Unit, Children’s Hospital Colorado, Tenured Professor of Pediatrics, Pediatric Cardiology and Intensive Care, University of Colorado Denver, School of Medicine, Aurora, CO, USA

    Eduardo M. da Cruz

  3. Department of Pediatric Radiology, Children’s Hospital Colorado, University of Colorado Denver School of Medicine, Aurora, CO, USA

    Jason P. Weinman

  4. Pediatric Cardiothoracic Surgery, Heart Institute, Children’s Hospital Colorado, University of Colorado Denver School of Medicine, Aurora, CO, USA

    James Jaggers

Authors
  1. Uyen Truong
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  2. Eduardo M. da Cruz
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  3. Jason P. Weinman
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  4. James Jaggers
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Corresponding author

Correspondence to Uyen Truong .

Editor information

Editors and Affiliations

  1. Chief, Division of Cardiac Critical Care Medicine Executive Director, Telemedicine Co-director, Children’s National Heart Institute, Professor of Pediatrics, George Washington University School of Medicine, Children’s National Health System, Washington, DC, USA

    Ricardo A. Munoz

  2. Department of Pediatric Cardiothoracic Surgery, UPMC Children’s Hospital of Pittsburgh, Pittsburgh, PA, USA

    Victor O. Morell

  3. Associate Medical Director, CHCO Heart Institute Head, Pediatric Cardiac Critical Care Program & Inpatient Services Director, Cardiac Intensive Care Unit Children’s Hospital Colorado, Tenured Professor of Pediatrics, Pediatric Cardiology and Intensive Care University of Colorado Denver, School of Medicine, Aurora, CO, USA

    Eduardo M. da Cruz

  4. Department of Pharmacy, Pediatric Critical Care, UPMC Children’s Hospital of Pittsburgh, Pittsburgh, PA, USA

    Carol G. Vetterly

  5. Department of Pediatric Cardiothoracic Surgery, UPMC – Children’s Hospital of Pittsburgh, Pittsburgh, PA, USA

    Jose Pedro da Silva

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Truong, U., da Cruz, E.M., Weinman, J.P., Jaggers, J. (2020). Double Outlet Right Ventricle. In: Munoz, R., Morell, V., da Cruz, E., Vetterly, C., da Silva, J. (eds) Critical Care of Children with Heart Disease . Springer, Cham. https://doi.org/10.1007/978-3-030-21870-6_35

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  • DOI: https://doi.org/10.1007/978-3-030-21870-6_35

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-21869-0

  • Online ISBN: 978-3-030-21870-6

  • eBook Packages: MedicineMedicine (R0)

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