Skip to main content
SpringerLink
Log in

Truncus Arteriosus

  • Chapter
  • First Online:
Critical Care of Children with Heart Disease

  • 1450 Accesses

Abstract

Truncus arteriosus is a rare congenital cardiac malformation with a reported incidence between 0.006 and 0.043 per 1000 live births. It accounts for 0.7% of all congenital cardiac malformations and for 1–2% of congenital heart diseases identified at autopsies. This malformation has been defined as an anomaly in which the aorta, the coronary arteries, and the pulmonary arteries arise from a single vessel (common truncus) originated from the cardiac chambers. There is no remnant or rudimentary pulmonary artery arising separately from the heart. This chapter reviews the diagnosis and management of this entity.

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

Log in via an institution
Chapter
USD 29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD 109.00
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD 139.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info
Hardcover Book
USD 199.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

References

  1. Perloff JK. Truncus arteriosus. In: Perloff JK. The Clinical Recognition of Congenital Heart Disease. 4th ed. Philadelphia, PA: WB Saunders; 1994:686–702.

    Google Scholar 

  2. Momma K, Matsuoka R, Takao A. Aortic arch anomalies associated with chromosome 22q11 deletion (CATCH 22). Pediatr Cardiol. 1999;20:97–102.

    Article  CAS  Google Scholar 

  3. Radford DJ, Perkins L, Lachman R, Thong Y. Spectrum of Di George syndrome in patients with truncus arteriosus: expanded Di George syndrome. Pediatr Cardiol. 1988;9:95–101.

    Article  CAS  Google Scholar 

  4. Van Praagh R, Van Praagh S. The anatomy of common aorticopulmonary trunk (truncus arteriosus communis) and its embryologic implications. A study of 57 necropsy cases. Am J Cardiol. 1965;16:406–425.

    Article  CAS  Google Scholar 

  5. Calder L, Van Praagh R, Van Praagh S, et al. Truncus arteriosus communis. Clinical, angiocardiographic, and pathologic findings in 100 patients. Am Heart J. 1976;92:23–38.

    Article  CAS  Google Scholar 

  6. Mair DD, Edwards WD, Julsrud PR, et al. Truncus arteriosus: congenital cardiovascular defects. In: Moss AJ, Adams FH, eds. Heart Disease in Infants, Children and Adolescents, Including the Fetus and Young Adults. 5th ed. Baltimore, MD: Lippincott Williams & Wilkins; 1995:1026–1041.

    Google Scholar 

  7. Butto F, Lucas RV Jr, Edwards JE. Persistent truncus arteriosus: pathologic anatomy in 54 cases. Pediatr Cardiol. 1986;7:95–101.

    Article  CAS  Google Scholar 

  8. Crupi G, Macartney FJ, Anderson RH. Persistent truncus arteriosus. A study of 66 autopsy cases with special reference to definition and morphogenesis. Am J Cardiol. 1977;40:569–578.

    Article  CAS  Google Scholar 

  9. Mair DD, Ritter DG, Davis GD, et al. Selection of patients with truncus arteriosus for surgical correction; anatomic and hemodynamic considerations. Circulation. 1974;49:144–151.

    Article  CAS  Google Scholar 

  10. Marino B, Ballerini L, Soro A. Ventricular inversion with truncus arteriosus. Chest. 1990;98:239–241.

    Article  CAS  Google Scholar 

  11. Gumbiner CH, McManus BM, Latson LA. Associated occurrence of persistent truncus arteriosus and asplenia. Pediatr Cardiol. 1991;12:192–195.

    Article  CAS  Google Scholar 

  12. Rao PS, Levy JM, Nikicicz E, Gilbert-Barness EF. Tricuspid atresia: association with persistent truncus arteriosus. Am Heart J. 1991;122:829–835.

    Article  CAS  Google Scholar 

  13. Rice MJ, Andrilenas K, Reller MD, McDonald RW. Truncus arteriosus associated with mitral atresia and a hypoplastic left ventricle. Pediatr Cardiol. 1991;12:128–130.

    Article  CAS  Google Scholar 

  14. Collet RW, Edwards JE. Persistent truncus arteriosus. A classification according to anatomic subtypes. Surg Clin North Am. 1949;29:1245.

    Article  Google Scholar 

  15. Rothko K, Moore GW, Hutchins GM. Truncus arteriosus malformation: a spectrum including fourth and sixth aortic arch interruptions. Am Heart J. 1980;99:17–24.

    Article  CAS  Google Scholar 

  16. Rosenquist GC, Bharati S, McAllister HA, Lev M. Truncus arteriosus communis: truncal valve anomalies associated with small conal or truncal septal defects. Am J Cardiol. 1976;37:410–412.

    Article  CAS  Google Scholar 

  17. Marcelletti C, McGoon DC, Mair DD. The natural history of truncus arteriosus. Circulation. 1976;54:108–111.

    Article  CAS  Google Scholar 

  18. Didier D, Ratib O, Beghetti M, et al. Morphologic and functional evaluation of congenital heart disease by magnetic resonance imaging. J Magn Reson Imaging. 1999;10:639–655.

    Article  CAS  Google Scholar 

  19. Barbero-Marcial M, Riso A, Atik E, Jatene A. A technique for correction of truncus arteriosus types I and II without extracardiac conduits. J Thorac Cardiovasc Surg. 1990;99:364–369.

    Article  CAS  Google Scholar 

  20. Vouhé P. Tronc artériel commun: traitement chirurgical. Encycl Med Chir (Elsevier, Paris), Techniques Chirurgicales-Thorax. 1998;42:825–838.

    Google Scholar 

  21. Chiu I, Wu M, Ming-Ren C, Shyh-Jye C, Wang J. Anatomic relationship of the coronary orifice and truncal valve in truncus arteriosus and their surgical implication. J Thorac Cardiovasc Surg. 2002;123:350–352.

    Article  Google Scholar 

  22. Brizard C, Cochrane A, Austin C, Nomura F, Karl T. Management strategy and long term outcome for truncus arteriosus. Eur J Cardio-thorac Surg. 1997;11:687–696.

    Article  CAS  Google Scholar 

  23. Williams JM, de Leeuw M, Black MD, Freedom RM, Williams WG, McCrindle BW. Factors associated with outcomes of persistent truncus arteriosus. J Am Coll Cardiol. 1999;34:545–553.

    Article  CAS  Google Scholar 

  24. Thompson L, McElhinney D, Reddy V, Petrossian E, Silverman N, Hanley F. Neonatal repair of truncus arteriosus: continuing improvement in outcomes. Ann Thorac Surg. 2001;72:391–395.

    Article  CAS  Google Scholar 

  25. Brown JW, Ruzmetov M, Okada Y, Vijay P, Turrentine MW. Truncus arteriosus repair: outcomes, risk factors, reoperation and management. Eur J Cardiothorac Surg. 2001;20:221–227.

    Article  CAS  Google Scholar 

  26. Ullman M, Gorenflo M, Sebening C, Ulmer H, Hagl S. Long Term results after repair of truncus arteriosus communis in neonates and infants. J Thorac Cardiovasc Surg. 2003;53:175–179.

    Google Scholar 

  27. Bove EL, Lupinetti FM, Pridjian AK, Beekman RH, Callow LB et al. Results of a policy of primary repair of truncus arteriosus in the neonate. J Thorac Cardiovasc Surg. 1993;105:1057–1066.

    Article  CAS  Google Scholar 

  28. Hanley FL, Heinemann MK, Jonas RA, Mayer JE, Cook NR et al. Repair of truncus arteriosus in the neonate. J Thorac Cardiovasc Surg. 1993;105:1047–1056.

    Article  CAS  Google Scholar 

  29. Lacour-Gayet F, Serraf A, Komiya T, Sousa-Uva M, Bruniaux J et al. Truncus arteriosus repair: influence of techniques of right ventricular outflow tract reconstruction. J Thorac Cardiovasc Surg. 1996;111:849–856.

    Article  CAS  Google Scholar 

  30. Rajasinghe HA, McElhinney DB, Reddy VM, Mora BN, Hanley FL. Long-term follow-up of truncus arteriosus repaired in infancy: a twenty-year experience. J Thorac Cardiovasc Surg. 1997;113:869–879.

    Article  CAS  Google Scholar 

  31. Hicken P, Evans D, Heath D. Persistent truncus arteriosus with survival to the age of 38 years. Br Heart J. 1966;28:284–286.

    Article  CAS  Google Scholar 

  32. Silverman JJ, Scheinesson GP. Persistent truncus arteriosus in a 43 year old man. Am J Cardiol. 1966;17:94–96.

    Article  CAS  Google Scholar 

Download references

Author information

Authors and Affiliations

  1. Associate Medical Director, CHCO Heart Institute, Head, Pediatric Cardiac Critical Care Program & Inpatient Services, Director, Cardiac Intensive Care Unit, Children’s Hospital Colorado, Tenured Professor of Pediatrics, Pediatric Cardiology and Intensive Care, University of Colorado Denver, School of Medicine, Aurora, CO, USA

    Eduardo M. da Cruz

  2. Pediatric Cardiovascular Surgery, University of Pittsburgh Medical Center, Wolfson Children’s Hospital, Jacksonville, FL, USA

    Harma K. Turbendian

  3. Department of Pediatric Cardiothoracic Surgery, UPMC Children’s Hospital of Pittsburgh, Pittsburgh, PA, USA

    Victor O. Morell

Authors
  1. Eduardo M. da Cruz
    View author publications

    You can also search for this author in PubMed Google Scholar

  2. Harma K. Turbendian
    View author publications

    You can also search for this author in PubMed Google Scholar

  3. Victor O. Morell
    View author publications

    You can also search for this author in PubMed Google Scholar

Corresponding author

Correspondence to Eduardo M. da Cruz .

Editor information

Editors and Affiliations

  1. Chief, Division of Cardiac Critical Care Medicine Executive Director, Telemedicine Co-director, Children’s National Heart Institute, Professor of Pediatrics, George Washington University School of Medicine, Children’s National Health System, Washington, DC, USA

    Ricardo A. Munoz

  2. Department of Pediatric Cardiothoracic Surgery, UPMC Children’s Hospital of Pittsburgh, Pittsburgh, PA, USA

    Victor O. Morell

  3. Associate Medical Director, CHCO Heart Institute Head, Pediatric Cardiac Critical Care Program & Inpatient Services Director, Cardiac Intensive Care Unit Children’s Hospital Colorado, Tenured Professor of Pediatrics, Pediatric Cardiology and Intensive Care University of Colorado Denver, School of Medicine, Aurora, CO, USA

    Eduardo M. da Cruz

  4. Department of Pharmacy, Pediatric Critical Care, UPMC Children’s Hospital of Pittsburgh, Pittsburgh, PA, USA

    Carol G. Vetterly

  5. Department of Pediatric Cardiothoracic Surgery, UPMC – Children’s Hospital of Pittsburgh, Pittsburgh, PA, USA

    Jose Pedro da Silva

Rights and permissions

Reprints and permissions

Copyright information

© 2020 Springer Nature Switzerland AG

About this chapter

Check for updates. Verify currency and authenticity via CrossMark

Cite this chapter

da Cruz, E.M., Turbendian, H.K., Morell, V.O. (2020). Truncus Arteriosus. In: Munoz, R., Morell, V., da Cruz, E., Vetterly, C., da Silva, J. (eds) Critical Care of Children with Heart Disease . Springer, Cham. https://doi.org/10.1007/978-3-030-21870-6_34

Download citation

  • DOI: https://doi.org/10.1007/978-3-030-21870-6_34

  • Published:

  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-21869-0

  • Online ISBN: 978-3-030-21870-6

  • eBook Packages: MedicineMedicine (R0)

Publish with us

Policies and ethics

Search

Navigation