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Pneumocystis jiroveci Pneumonia Without Failure to Thrive

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Abstract

  • A normal development and lymphocyte count do not exclude a combined immunodeficiency

  • All males with Pneumocystis jirovecii pneumonia, hypogammaglobulinemia with normal IgM must be tested for CD40L deficiency

  • Allogeneic hematopoietic stem cell transplantation is the only curative treatment currently available in CD40L deficiency and must be performed prior to the onset of a life-threatening complication and end organ damage

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Bataneant, M.T., Urtila, P. (2019). Pneumocystis jiroveci Pneumonia Without Failure to Thrive. In: Rezaei, N. (eds) Pediatric Immunology. Springer, Cham. https://doi.org/10.1007/978-3-030-21262-9_42

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  • DOI: https://doi.org/10.1007/978-3-030-21262-9_42

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-21261-2

  • Online ISBN: 978-3-030-21262-9

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