Abstract
Peripheral nerve sheath tumors of the uveal tract arise mainly in the sheath of peripheral nerves that are found in the uvea. The ciliary nerve is most often affected, and hence these tumors tend to be located anteriorly, in the ciliary body or peripheral choroid in the anatomic location of the long ciliary nerve. There are several systemic predisposing risk factors, which include schwannomatosis, neurofibromatosis 1 (NF1) and 2, and other rare genetic syndromes. The benign tumors can be subclassified as neurofibroma and schwannoma. The malignant nerve sheath tumors are more difficult to subclassify if they lose the histological characteristics of their benign counterparts. In this chapter, we discuss uveal neurofibroma and schwannoma.
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Cohen, V.M.L., Damato, B.E., Singh, A.D. (2019). Uveal Neural Tumors. In: Damato, B., Singh, A. (eds) Clinical Ophthalmic Oncology. Springer, Cham. https://doi.org/10.1007/978-3-030-17879-6_24
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DOI: https://doi.org/10.1007/978-3-030-17879-6_24
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