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The Pediatric and Adolescent Hip pp 715–734Cite as

The Hip in Osteogenesis Imperfecta

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Abstract

Osteogenesis imperfecta (OI) can cause fractures and progressive deformity of the bones of the pelvis and hip joint in addition to fractures of the long bones. In children with moderate to severe forms of the disease, coxa vara and acetabular protrusion occur quite commonly as do upper femoral shaft deformities and femoral neck fractures. A small subset of patients with the C-propeptide mutation will have an increased risk of hip dysplasia and dislocation as well. This chapter describes the clinical presentations, pathophysiology and treatment of coxa vara, acetabular protrusion, developmental hip dislocation, proximal femoral fractures and deformity in children with OI.

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Authors and Affiliations

  1. Orthopaedic Surgery, University of Nebraska Medical Center, Omaha, NE, USA

    Maegen Wallace & Paul Esposito

Authors
  1. Maegen Wallace
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  2. Paul Esposito
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Correspondence to Paul Esposito .

Editor information

Editors and Affiliations

  1. Clinical Director of Paediatric Trauma and Orthopaedic Surgery, Royal Manchester Children Hospital, Manchester University NHS Foundation Trust, Manchester, UK

    Sattar Alshryda

  2. Weill Cornell Medicine, Chief of Orthopaedic Surgery Sidra Medicine, Doha, Qatar

    Jason J. Howard

  3. Senior Attending Physician in Pediatric Orthopedic Surgery, Sidra Medicine, Doha, Qatar

    James S. Huntley

  4. Vanderbilt University Medical Center, Jeffrey Mast Chair of Orthopaedic Hip and Trauma Surgery, Nashville, TN, USA

    Jonathan G. Schoenecker

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Wallace, M., Esposito, P. (2019). The Hip in Osteogenesis Imperfecta. In: Alshryda, S., Howard, J., Huntley, J., Schoenecker, J. (eds) The Pediatric and Adolescent Hip. Springer, Cham. https://doi.org/10.1007/978-3-030-12003-0_29

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  • DOI: https://doi.org/10.1007/978-3-030-12003-0_29

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-12002-3

  • Online ISBN: 978-3-030-12003-0

  • eBook Packages: MedicineMedicine (R0)

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