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The Pediatric and Adolescent Hip pp 553–570Cite as

The Hip in Spinal Muscular Atrophy

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Abstract

The musculoskeletal burden of spinal muscular atrophy (SMA) primarily involves the hip and spine. The incidence of hip instability is 30–40% and neuromuscular scoliosis is 60–90% in non-ambulatory SMA patients. The intrinsic relationship between hip and spinal deformity often requires concomitant management of the hip and spine to maximize functional and clinical outcomes. This chapter summarizes the non-operative and operative treatments for hip instability and spinal deformity in the SMA population. While hip subluxation/dislocation has traditionally been treated non-operatively in non-ambulatory SMA patients, the intra-thecal administration of Nusinersen has changed the functional and ambulatory prognosis of patients with SMA. Thus, orthopedic surgeons should consider treating hip instability with operative hip reconstruction as the surgical complication and recurrence rate is similar to that in other neuromuscular conditions.

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Author information

Authors and Affiliations

  1. Ann & Robert H. Lurie Children’s Hospital of Chicago, Chicago, IL, USA

    Jill E. Larson

  2. Boston Children’s Hospital, Boston, MA, USA

    Brian Snyder

Authors
  1. Jill E. Larson
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  2. Brian Snyder
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Correspondence to Jill E. Larson .

Editor information

Editors and Affiliations

  1. Clinical Director of Paediatric Trauma and Orthopaedic Surgery, Royal Manchester Children Hospital, Manchester University NHS Foundation Trust, Manchester, UK

    Sattar Alshryda

  2. Weill Cornell Medicine, Chief of Orthopaedic Surgery Sidra Medicine, Doha, Qatar

    Jason J. Howard

  3. Senior Attending Physician in Pediatric Orthopedic Surgery, Sidra Medicine, Doha, Qatar

    James S. Huntley

  4. Vanderbilt University Medical Center, Jeffrey Mast Chair of Orthopaedic Hip and Trauma Surgery, Nashville, TN, USA

    Jonathan G. Schoenecker

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Larson, J.E., Snyder, B. (2019). The Hip in Spinal Muscular Atrophy. In: Alshryda, S., Howard, J., Huntley, J., Schoenecker, J. (eds) The Pediatric and Adolescent Hip. Springer, Cham. https://doi.org/10.1007/978-3-030-12003-0_20

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  • DOI: https://doi.org/10.1007/978-3-030-12003-0_20

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-12002-3

  • Online ISBN: 978-3-030-12003-0

  • eBook Packages: MedicineMedicine (R0)

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