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Genetic Generalized Epilepsies

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Clinical Electroencephalography

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Abstract

The purpose of this chapter is to delineate the clinical and EEG features of the genetic generalized epilepsies, which are a heterogeneous group of conditions, linked by strict criteria. Both the EEG and seizure characteristics may be helpful in the clinical management of patients and avoid unuseful therapies and diagnostic procedures.

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Author information

Authors and Affiliations

  1. Department of Health Sciences, Epilepsy Center—Child and Adolescent Neurology and Psychiatry, University of Milan, Milan, Italy

    Aglaia Vignoli & Maria Paola Canevini

Authors
  1. Aglaia Vignoli
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  2. Maria Paola Canevini
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Correspondence to Aglaia Vignoli .

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Editors and Affiliations

  1. Department of Human Neurosciences, Sapienza University of Rome, Rome, Italy

    Oriano Mecarelli

1 Electronic Supplementary Material

In the video, the girl has an initial brief eyelid flickering; she remains completely unresponsive from the beginning to the terminal phase of the discharge (MP4 10078 kb)

Video recording of a child with CAE: the ictal discharge is related to a complete loss of awareness and automatisms, which end at the end of the seizure (MP4 9758 kb)

JME ictal recording of a 9-year-old boy at morning awakening. Several generalized PSW discharges associated with bilateral jerks are recorded (MP4 6914 kb)

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Vignoli, A., Canevini, M.P. (2019). Genetic Generalized Epilepsies. In: Mecarelli, O. (eds) Clinical Electroencephalography. Springer, Cham. https://doi.org/10.1007/978-3-030-04573-9_27

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  • DOI: https://doi.org/10.1007/978-3-030-04573-9_27

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