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Non-atherosclerotic and non-vasculitic diseases

  • Chapter
The Pathology of Vessels

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Abstract

First reported by Leadbetter and Burkland in 1938 [1], fibromuscular dysplasia (FMD) is a segmental, non-atheromatous and non-inflammatory disease affecting mostly intermediate size arteries. It is manifest by consistent alterations in the smooth muscle cells of arteries, associated with modifications of the extracellular ground substance. Recent progress in diagnostic imaging allows more precise diagnosis of the location and type of lesions and, in general, pathologists have few opportunities to study fibromuscular dysplasia. X-ray-controlled angioplasty or embolization [2–4] now deals with most of the lesions and operative surgery is carried out only when angioplasty fails. The morphological pattern of fibromuscular dysplasia now seen by the pathologist is a mixture of the primary lesions plus the changes produced by the complications of angioplasty. Many so-called natural complications (dissecting haematoma, aneurysm, AV fistula) result directly from the invasive techniques.

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Authors and Affiliations

  1. Unité d’anatomie et de Cytologie Pathologiques, Hôpital Saint-Michel, 33, rue Olivier-de-Serres, 75015, Paris, France

    Phat N. Vuong MD, PhD, DHDR

  2. Department of Morbid Anatomy and Histopathology, St. Bartholomew’s and the Royal London School of Medecine and Dentistry, E1 1BB, Whitechapel, London, UK

    Sir Colin Berry DSc, MD, PhD, FRCPath, FRCP, FFPM

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  1. Phat N. Vuong MD, PhD, DHDR
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  2. Sir Colin Berry DSc, MD, PhD, FRCPath, FRCP, FFPM
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Vuong, P.N., Berry, C. (2002). Non-atherosclerotic and non-vasculitic diseases. In: The Pathology of Vessels. Springer, Paris. https://doi.org/10.1007/978-2-8178-0786-7_5

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  • DOI: https://doi.org/10.1007/978-2-8178-0786-7_5

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