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Developmental anomalies and hereditary diseases of vessels

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Book cover The Pathology of Vessels

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Abstract

Congenital vascular anomalies can be divided into three groups: those developing during intra-uterine life, those associated with karyotype aberrations, and those arising from the effects of single genes or complex polygenic mutations. There are no good data on the incidence of these lesions; a recent Finnish study on 4346 new-borns showed a 3.8% rate of vascular lesions excluding salmon patches on the head and neck, in general agreement with other studies [1]. Seventy to 80% of lesions are said to regress spontaneously by the age of seven years. In most instances of this type of lesion both blood and lymphatic vessels may be affected.

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Authors and Affiliations

  1. Unité d’anatomie et de Cytologie Pathologiques, Hôpital Saint-Michel, 33, rue Olivier-de-Serres, 75015, Paris, France

    Phat N. Vuong MD, PhD, DHDR

  2. Department of Morbid Anatomy and Histopathology, St. Bartholomew’s and the Royal London School of Medecine and Dentistry, E1 1BB, Whitechapel, London, UK

    Sir Colin Berry DSc, MD, PhD, FRCPath, FRCP, FFPM

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  1. Phat N. Vuong MD, PhD, DHDR
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  2. Sir Colin Berry DSc, MD, PhD, FRCPath, FRCP, FFPM
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© 2002 Springer-Verlag France

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Vuong, P.N., Berry, C. (2002). Developmental anomalies and hereditary diseases of vessels. In: The Pathology of Vessels. Springer, Paris. https://doi.org/10.1007/978-2-8178-0786-7_14

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  • DOI: https://doi.org/10.1007/978-2-8178-0786-7_14

  • Publisher Name: Springer, Paris

  • Print ISBN: 978-2-8178-0788-1

  • Online ISBN: 978-2-8178-0786-7

  • eBook Packages: Springer Book Archive

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