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Arrhythmias and Sudden Cardiac Death in Adult Congenital Heart Disease

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Clinical Approach to Sudden Cardiac Death Syndromes

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Abstract

Congenital heart disease is the leading category of birth defects, afflicting an estimated 75 of 1,000 live newborns, 25% of whom have moderate or severe disease.1 Over the last half century, the field of congenital heart disease has witnessed extraordinary strides. Whereas, decades ago, a minority of children with congenital heart defects survived to adulthood, current estimates project that 95% will prosper into their adult years.2-4 As a product of this astounding progress, the population of patients with congenital heart disease is rapidly growing and aging.5 Compellingly, adults now outnumber children with congenital heart disease.6

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Acknowledgments

This work was supported in part by the Canada Research Chair in Electrophysiology and Adult Congenital Heart Disease.

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  1. Montreal Heart Institute, University of Montreal, Montreal, QC, Canada, H3A 1A1

    Paul Khairy

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    Ramon Brugada

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Khairy, P. (2010). Arrhythmias and Sudden Cardiac Death in Adult Congenital Heart Disease. In: Brugada, R. (eds) Clinical Approach to Sudden Cardiac Death Syndromes. Springer, London. https://doi.org/10.1007/978-1-84882-927-5_4

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