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Infiltrative Cardiomyopathy

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The ESC Textbook of Cardiovascular Imaging

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Abstract

Infiltrative cardiomyopathy can result from a wide spectrum of both inherited and acquired conditions with varying systemic manifestations. They usually portend an adverse prognosis, although in rare instances (e.g. Fabry’s disease) early diagnosis can result in potentially curative treatment. Cardiac amyloid remains the archetypal infiltrative cardiomyopathy and is discussed in great detail in this chapter. Non-invasive imaging modalities, principally echocardiography and cardiovascular magnetic resonance (CMR), play a pivotal role in the early diagnosis and management of all types of infiltrative cardiomyopathy.

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Author information

Authors and Affiliations

  1. Department of Cardiovascular Medicine, Flinders Medical Center, Flinders Drive, Bedford Park, Adelaide, Australia, 5042

    Joseph B. Selvanayagam

Authors
  1. Joseph B. Selvanayagam
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  2. Majo Joseph
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  3. Stefan Neubauer
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Corresponding author

Correspondence to Joseph B. Selvanayagam .

Editor information

Editors and Affiliations

  1. Hospital Clinico San Carlos, Instituto Cardiovascular, C/Professor Martin Lagos, s/n, 28040, Madrid, Spain

    José Luis Zamorano

  2. Medical Center Dept. Cardiology, Leiden University, Albinusdreef 2, 2333, Leiden, ZA, Netherlands

    Jeroen J. Bax

  3. Dept. Cardiology, University Hospitals Leuven, Herestraat 49, 3000, Leuven, Belgium

    Frank E. Rademakers

  4. Turku PET Centre, Turku University Hospital, FI-20521, Turku, Finland

    Juhani Knuuti

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Selvanayagam, J.B., Joseph, M., Neubauer, S. (2010). Infiltrative Cardiomyopathy. In: Zamorano, J.L., Bax, J.J., Rademakers, F.E., Knuuti, J. (eds) The ESC Textbook of Cardiovascular Imaging. Springer, London. https://doi.org/10.1007/978-1-84882-421-8_23

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  • DOI: https://doi.org/10.1007/978-1-84882-421-8_23

  • Publisher Name: Springer, London

  • Print ISBN: 978-1-84882-420-1

  • Online ISBN: 978-1-84882-421-8

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