Skip to main content
SpringerLink
Log in

Truncus Arteriosus

  • Chapter
  • First Online:
Critical Care of Children with Heart Disease

  • 3807 Accesses

Abstract

Truncus Arteriosus (TA) is a rare congenital cardiac malformation, firstly described by Wilson in 1798 and reported with an incidence between 0.006 and 0.043 per 1,000 live births. It accounts for 0.7% of all congenital cardiac malformations [1] and for 1–2% of congenital heart diseases identified at autopsies. This disease occurs with equal frequency in male and female gender and it has no racial preference.

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

Log in via an institution
Chapter
USD 29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD 149.00
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD 199.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

References and Further Reading

  1. Perloff JK. Truncus arteriosus. In: Perloff JK, ed. The Clinical Recognition of Congenital Heart Disease. 4th ed. Philadelphia, PA: WB Saunders; 1994:686–702.

    Google Scholar 

  2. Momma K, Matsuoka R, Takao A. Aortic arch anomalies associated with chromosome 22q11 deletion (CATCH 22). Pediatr Cardiol. 1999;20:97–102.

    Article  PubMed  CAS  Google Scholar 

  3. Radford DJ, Perkins L, Lachman R, Thong Y. Spectrum of Di George syndrome in patients with truncus arteriosus: expanded Di George syndrome. Pediatr Cardiol. 1988;9:95–101.

    Article  PubMed  CAS  Google Scholar 

  4. Van Praagh R, Van Praagh S. The anatomy of common aorticopulmonary trunk (truncus arteriosus communis) and its embryologic implications. A study of 57 necropsy cases. Am J Cardiol. 1965;16:406–425.

    Article  PubMed  Google Scholar 

  5. Calder L, Van Praagh R, Van Praagh S, et al. Truncus arteriosus communis. Clinical, angiocardiographic, and pathologic findings in 100 patients. Am Heart J. 1976;92:23–38.

    Article  PubMed  CAS  Google Scholar 

  6. Mair DD, Edwards WD, Julsrud PR, et al. Truncus arteriosus: congenital cardiovascular defects. In: Moss AJ, Adams FH, eds. Heart Disease in Infants, Children and Adolescents, Including the Fetus and Young Adults. 5th ed. Baltimore, MD: Lippincott Williams & Wilkins; 1995:1026–1041.

    Google Scholar 

  7. Butto F, Lucas RV Jr, Edwards JE. Persistent truncus arteriosus: pathologic anatomy in 54 cases. Pediatr Cardiol. 1986;7:95–101.

    Article  PubMed  CAS  Google Scholar 

  8. Crupi G, Macartney FJ, Anderson RH. Persistent truncus arteriosus. A study of 66 autopsy cases with special reference to definition and morphogenesis. Am J Cardiol. 1977;40:569–578.

    Article  PubMed  CAS  Google Scholar 

  9. Mair DD, Ritter DG, Davis GD, et al. Selection of patients with truncus arteriosus for surgical correction; anatomic and hemodynamic considerations. Circulation. 1974;49:144–151.

    Article  PubMed  CAS  Google Scholar 

  10. Marino B, Ballerini L, Soro A. Ventricular inversion with truncus arteriosus. Chest. 1990;98:239–241.

    Article  PubMed  CAS  Google Scholar 

  11. Gumbiner CH, McManus BM, Latson LA. Associated occurrence of persistent truncus arteriosus and asplenia. Pediatr Cardiol. 1991;12:192–195.

    Article  PubMed  CAS  Google Scholar 

  12. Rao PS, Levy JM, Nikicicz E, Gilbert-Barness EF. Tricuspid atresia: association with persistent truncus arteriosus. Am Heart J. 1991;122:829–835.

    Article  PubMed  CAS  Google Scholar 

  13. Rice MJ, Andrilenas K, Reller MD, McDonald RW. Truncus arteriosus associated with mitral atresia and a hypoplastic left ventricle. Pediatr Cardiol. 1991;12:128–130.

    Article  PubMed  CAS  Google Scholar 

  14. Collet RW, Edwards JE. Persistent truncus arteriosus. A classification according to anatomic subtypes. Surg Clin North Am. 1949;29:1245.

    Google Scholar 

  15. Rothko K, Moore GW, Hutchins GM. Truncus arteriosus malformation: a spectrum including fourth and sixth aortic arch interruptions. Am Heart J. 1980;99:17–24.

    Article  PubMed  CAS  Google Scholar 

  16. Rosenquist GC, Bharati S, McAllister HA, Lev M. Truncus arteriosus communis: truncal valve anomalies associated with small conal or truncal septal defects. Am J Cardiol. 1976;37:410–412.

    Article  PubMed  CAS  Google Scholar 

  17. Marcelletti C, McGoon DC, Mair DD. The natural history of truncus arteriosus. Circulation. 1976;54:108–111.

    Article  PubMed  CAS  Google Scholar 

  18. Didier D, Ratib O, Beghetti M, et al. Morphologic and functional evaluation of congenital heart disease by magnetic resonance imaging. J Magn Reson Imaging. 1999;10:639–655.

    Article  PubMed  CAS  Google Scholar 

  19. Barbero-Marcial M, Riso A, Atik E, Jatene A. A technique for correction of truncus arteriosus types I and II without extracardiac conduits. J Thorac Cardiovasc Surg. 1990;99:364–369.

    PubMed  CAS  Google Scholar 

  20. Vouhé. Tronc artériel commun: traitement chirurgical. Encycl Med Chir (Elsevier, Paris). Techniques Chirurgicales-Thorax. 1998;42:825–838.

    Google Scholar 

  21. Bove EL, Lupinetti FM, Pridjian AK, Beekman RH, Callow LB, et al. Results of a policy of primary repair of truncus arteriosus in the neonate. J Thorac Cardiovasc Surg. 1993;105:1057–1066.

    PubMed  CAS  Google Scholar 

  22. Hanley FL, Heinemann MK, Jonas RA, Mayer JE, Cook NR, et al. Repair of truncus arteriosus in the neonate. J Thorac Cardiovasc Surg. 1993;105:1047–1056.

    PubMed  CAS  Google Scholar 

  23. Lacour-Gayet F, Serraf A, Komiya T, Sousa-Uva M, Bruniaux J, et al. Truncus arteriosus repair: influence of techniques of right ventricular outflow tract reconstruction. J Thorac Cardiovasc Surg. 1996;111:849–856.

    Article  PubMed  CAS  Google Scholar 

  24. Rajasinghe HA, McElhinney DB, Reddy VM, Mora BN, Hanley FL. Long-term follow-up of truncus arteriosus repaired in infancy: a twenty-year experience. J Thorac Cardiovasc Surg. 1997;113:869–879.

    Article  PubMed  CAS  Google Scholar 

  25. Hicken P, Evans D, Heath D. Persistent truncus arteriosus with survival to the age of 38 years. Br Heart J. 1966;28:284–286.

    Article  PubMed  CAS  Google Scholar 

  26. Silverman JJ, Scheinesson GP. Persistent truncus arteriosus in a 43 year old man. Am J Cardiol. 1966;17:94–96.

    Article  PubMed  CAS  Google Scholar 

  27. Jonas R. Truncus arteriosus. In: Jonas R, ed. Comprehensive Surgical Management of Congenital Heart Disease. 1st ed. Grean Britain: Arnold; 2004:429–439.

    Chapter  Google Scholar 

  28. Keane J, Fyler D. Truncus arteriosus. In: Keane J, Lock J, Fyler D, eds. Nadas’ Pediatric Cardiology. 2nd ed. Philadelphia, PA: Saunders Elsevier; 2006:767–771.

    Google Scholar 

  29. Chiu I, Wu M, Ming-Ren C, Shyh-Jye C, Wang J. Anatomic relationship of the coronary orifice and truncal valve in truncus arteriosus and their surgical implication. J Thorac Cardiovasc Surg. 2002;123:350–352.

    Article  PubMed  Google Scholar 

  30. Hosseinpour A, Shinebourne E. Assessment of operability for common arterial trunk without cardiac catheterization. Cardiol Young. 2005;15:241–244.

    Article  PubMed  Google Scholar 

  31. Pigula F, Mahnke B, Agnastopolous P, Casta A, Muñoz R, Gandhi S. Closed correction of systemic semilunar valve insufficiency in the neonate. J Thorac Cardiovasc Surg. 2003;126:1650–1652.

    Article  PubMed  Google Scholar 

  32. Haydar S. Lecompte maneuver in truncus arteriosus repair: potential risks!. Ann Thorac Surg. 1996;62:1241.

    Article  PubMed  CAS  Google Scholar 

  33. Brizard C, Cochrane A, Austin C, Nomura F, Karl T. Management strategy and long term outcome for truncus arteriosus. Eur J Cardiothorac Surg. 1997;11:687–696.

    Article  PubMed  CAS  Google Scholar 

  34. Hanley FL, Heinemann MK, Jonas RA, et al. Repair of truncus arteriosus in the neonate. J Thorac Cardiovasc Surg. 1993;105:1047–1056.

    PubMed  CAS  Google Scholar 

  35. Williams JM, de Leeuw M, Black MD, Freedom RM, Williams WG, McCrindle BW. Factors associated with outcomes of persistent truncus arteriosus. J Am Coll Cardiol. 1999;34:545–553.

    Article  PubMed  CAS  Google Scholar 

  36. Jahangiri M, Zurakowski D, Mayer JE, del Nido PJ, Jonas RA. Repair of the truncal valve and associated interrupted arch in neonates with truncus arteriosus. J Thorac Cardiovasc Surg. 2000;119:508–514.

    Article  PubMed  CAS  Google Scholar 

  37. McElhinney DB, Rajasinghe HA, Mora BN, Reddy VM, Silverman NH, Hanley FL. Reinterventions after repair of common arterial trunk in neonates and young infants. J Am Coll Cardiol. 2000;35:1317–1322.

    Article  PubMed  CAS  Google Scholar 

  38. Thompson L, McElhinney D, Reddy V, Petrossian E, Silverman N, Hanley F. Neonatal repair of truncus arteriosus: continuing improvement in outcomes. Ann Thorac Surg. 2001;72:391–395.

    Article  PubMed  CAS  Google Scholar 

  39. Tlaskal T, Hucin B, Kucera V, et al. Repair of persistent truncus arteriosus with interrupted aortic arch. Eur J Cardiothorac Surg. 2005;28:736–741.

    Article  PubMed  Google Scholar 

  40. Brown JW, Ruzmetov M, Okada Y, Vijay P, Turrentine MW. Truncus arteriosus repair: outcomes, risk factors, reoperation and management. Eur J Cardiothorac Surg. 2001;20:221–227.

    Article  PubMed  CAS  Google Scholar 

  41. Mavroudis C, Backer CL. Surgical management of severe truncal insufficiency: experience with truncal valve remodeling techniques. Ann Thorac Surg. 2001;72:396–400.

    Article  PubMed  CAS  Google Scholar 

  42. McElhinney D, Reddy V, Brook M, Hanley F. Repair of truncus arteriosus with intact ventricular septum (Van Praagh type b2) in a neonate. J Thorac Cardiovasc Surg. 1997;114:134–138.

    Article  PubMed  CAS  Google Scholar 

  43. Ullman M, Gorenflo M, Sebening C, Ulmer H, Hagl S. Long Term results after repair of truncus arteriosus communis in neonates and infants. J Thorac Cardiovasc Surg. 2003;53:175–179.

    Google Scholar 

  44. Elzein C, Ilbawi M, Kumar S, Ruiz C. Severe truncal valve stenosis: diagnosis and management. J Card Surg. 2005;20:589–593.

    Article  PubMed  Google Scholar 

  45. Schreibera C, Eickenb A, Ballingb G, et al. Single centre experience on primary correction of common arterial trunk: overall survival and freedom from reoperation after more than 15 years. Eur J Cardiothorac Surg. 2000;18:68–73.

    Article  Google Scholar 

  46. Bengur A. Truncus arteriosus. In: Garson A, Bricker T, Fisher D, Neish S, eds. The Science and Practice of Pediatric Cardiology. 2nd ed. Baltimore, MD: Williams & Wilkins; 1998:1421–1430.

    Google Scholar 

  47. St Louis J. Persistent truncus arteriosus. In: Nichols D, Ungerleider R, eds. Critical Heart Disease in Infants and Children. 2nd ed. Philadelphia, PA: Mosby Elsevier; 2006:689–698.

    Chapter  Google Scholar 

Download references

Author information

Authors and Affiliations

  1. Pediatric Cardiology and Cardiac Intensive Care, Department of Pediatrics, The Children’s Hospital of Denver, Aurora, CO, USA

    Eduardo M. da Cruz

Authors
  1. Eduardo M. da Cruz
    View author publications

    You can also search for this author in PubMed Google Scholar

  2. Steven Goldberg
    View author publications

    You can also search for this author in PubMed Google Scholar

  3. Victor O. Morell
    View author publications

    You can also search for this author in PubMed Google Scholar

  4. Bertrand Léobon
    View author publications

    You can also search for this author in PubMed Google Scholar

  5. Mohammed Ly
    View author publications

    You can also search for this author in PubMed Google Scholar

  6. Chokri Kortas
    View author publications

    You can also search for this author in PubMed Google Scholar

  7. Alain Serraf
    View author publications

    You can also search for this author in PubMed Google Scholar

Corresponding author

Correspondence to Eduardo M. da Cruz .

Editor information

Editors and Affiliations

  1. Children's Hospital, Pittsburgh, 5th Ave. 3705, Pittsburgh, 15213, USA

    Ricardo Munoz

  2. School of Medicine, Children's Hospital, University of Pittsburgh, Fifth Ave. 3705, Pittsburgh, 15213, USA

    Victor Morell

  3. Chemin de Normanie 2, Geneve, 1206, Switzerland

    Eduardo Cruz

  4. Children's Hospital, Pittsburgh, 5th Ave. 3705, Pittsburgh, 15213, USA

    Carol Vetterly

Rights and permissions

Reprints and permissions

Copyright information

© 2009 Springer-Verlag London Limited

About this chapter

Cite this chapter

da Cruz, E.M. et al. (2009). Truncus Arteriosus. In: Munoz, R., Morell, V., Cruz, E., Vetterly, C. (eds) Critical Care of Children with Heart Disease. Springer, London. https://doi.org/10.1007/978-1-84882-262-7_35

Download citation

  • DOI: https://doi.org/10.1007/978-1-84882-262-7_35

  • Published:

  • Publisher Name: Springer, London

  • Print ISBN: 978-1-84882-261-0

  • Online ISBN: 978-1-84882-262-7

  • eBook Packages: MedicineMedicine (R0)

Publish with us

Policies and ethics

Search

Navigation