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Critical Care of Children with Heart Disease pp 231–240Cite as

Pulmonary Stenosis

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Abstract

Pulmonic stenosis refers to an obstruction at or distal to the right ventricular outflow. Owing to various possible levels of obstruction, this disease is not a homogeneous entity. Obstruction can be found at the valvar level, the right ventricular (RV) infundibulum, and/or the supravalvular level within the main pulmonary artery or distal to it at multiple levels. It is also found in association with ventricular septal defect and overriding aorta as in Tetralogy of Fallot (TOF) (see associated chapter). In patients suffering from congenital heart disease, 25–30% suffer from some form of pulmonary stenosis [1].

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Author information

Authors and Affiliations

  1. Pediatric Cardiovascular Intensive Care Unit, Sanger Clinic, Levine Children’s Hospital, Charlotte, NC, USA

    Yuliya A. Domnina

Authors
  1. Yuliya A. Domnina
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  2. Ricardo Muñoz
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  3. Jackie Kreutzer
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  4. Victor O. Morell
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Corresponding author

Correspondence to Yuliya A. Domnina .

Editor information

Editors and Affiliations

  1. Children's Hospital, Pittsburgh, 5th Ave. 3705, Pittsburgh, 15213, USA

    Ricardo Munoz

  2. School of Medicine, Children's Hospital, University of Pittsburgh, Fifth Ave. 3705, Pittsburgh, 15213, USA

    Victor Morell

  3. Chemin de Normanie 2, Geneve, 1206, Switzerland

    Eduardo Cruz

  4. Children's Hospital, Pittsburgh, 5th Ave. 3705, Pittsburgh, 15213, USA

    Carol Vetterly

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© 2009 Springer-Verlag London Limited

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Domnina, Y.A., Muñoz, R., Kreutzer, J., Morell, V.O. (2009). Pulmonary Stenosis. In: Munoz, R., Morell, V., Cruz, E., Vetterly, C. (eds) Critical Care of Children with Heart Disease. Springer, London. https://doi.org/10.1007/978-1-84882-262-7_23

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  • DOI: https://doi.org/10.1007/978-1-84882-262-7_23

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-84882-261-0

  • Online ISBN: 978-1-84882-262-7

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