Abstract
Aortopulmonary (AP) window, a communication between the ascending aorta and the pulmonary trunk in the presence of two separate arterial valves, is a relatively rare cardiac malformation, accounting for 0.1– 0.6% of all cases of congenital heart disease [1–6]. As the natural history of AP window is similar to that of a large ventricular septal defect (VSD) or a patent ductus arteriosus (PDA), early recognition is particularly important to allow for surgical closure before the development of pulmonary vascular obstructive disease (PVOD) [1, 3–6, 7–9]. AP windows do not close spontaneously, nor do they show diminution of size with time and growth [1, 3]. It is frequently (47–77% of cases) associated with other cardiac defects [1, 3, 4, 7, 9, 10]; including aortic origin of the right pulmonary artery, type A interruption of the aortic arch, right and double aortic arch, Tetralogy of Fallot, anomalous origin of the coronary arteries from the pulmonary artery, VSD, pulmonary or aortic atresia, transposition of the great arteries, and tricuspid atresia [1–3, 7, 8, 11–13].
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Moguillansky, D., Muñoz, R., Morell, V.O. (2009). Aortopulmonary Window. In: Munoz, R., Morell, V., Cruz, E., Vetterly, C. (eds) Critical Care of Children with Heart Disease. Springer, London. https://doi.org/10.1007/978-1-84882-262-7_18
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