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Complete Atrioventricular Septal Defects

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Critical Care of Children with Heart Disease

Abstract

Complete atrioventricular septal defect (CAVSD) refers to a complex malformation of the atrial and ventricular septum and is defined by an abnormal embryological development of the endocardial cushions in the atrioventricular canal resulting in maldevelopment of the atrial–ventricular valves [1]. CAVSD represents around 3% of congenital cardiac defects and it is a frequent anomaly in the context of autosomic trisomic anomalies, particularly in patients with Down’s syndrome (trisomy 21) and Edward’s syndrome (Trisomy 18). Fifty percent of atrioventricular septal defects are diagnosed in patients with Down’s syndrome and 30% of these have a CAVSD [2].

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Correspondence to Jonathan Kaufman .

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Kaufman, J. et al. (2009). Complete Atrioventricular Septal Defects. In: Munoz, R., Morell, V., Cruz, E., Vetterly, C. (eds) Critical Care of Children with Heart Disease. Springer, London. https://doi.org/10.1007/978-1-84882-262-7_17

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  • DOI: https://doi.org/10.1007/978-1-84882-262-7_17

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