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Management of Cardiac Arrhythmias pp 419–440Cite as

Long QT Syndrome

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Part of the book series: Contemporary Cardiology ((CONCARD))

Abstract

Over the past half century, LQTS has matriculated through several critical milestones including its sentinel clinical description, clinical diagnostic scorecard, pathogenetic discovery, decade of research-based genetic testing and genotype–phenotype correlations, and clinical availability of genetic testing. In this chapter, we will discuss the history, epidemiology, and clinical presentations of congenital long QT syndrome (LQTS). We will clarify current diagnostic approaches to LQTS, including clinical history and specific diagnostic testing. Treatment strategies including pharmacologic and surgical techniques will be examined, as well as the role of individualized treatment for the LQTS patient. Finally, preventative strategies will be discussed, including athletic participation.

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Authors and Affiliations

  1. Department of Pediatrics, Division of Pediatric Cardiology, Mayo Clinic, Rochester, MN, USA

    Jonathan N. Johnson MD

  2. Departments of Medicine, Pediatrics, and Molecular Pharmacology & Experimental Therapeutics/Divisions of Cardiovascular Diseases and Pediatric Cardiology/Windland Smith Rice Sudden Death Genomics Laboratory, Mayo Clinic, Rochester, MN, USA

    Michael J. Ackerman MD, PHD

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  1. Jonathan N. Johnson MD
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  2. Michael J. Ackerman MD, PHD
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Editors and Affiliations

  1. Main Line Health Heart Center, 100 Lancaster Ave, Wynnewood, 19096, Pennsylvania, USA

    Gan-Xin Yan

  2. Main Line Health Heart Center, 100 Lancaster Ave, Wynnewood, 19096, Pennsylvania, USA

    Peter R. Kowey

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Johnson, J.N., Ackerman, M.J. (2011). Long QT Syndrome. In: Yan, GX., Kowey, P. (eds) Management of Cardiac Arrhythmias. Contemporary Cardiology. Humana Press, Totowa, NJ. https://doi.org/10.1007/978-1-60761-161-5_19

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  • Publisher Name: Humana Press, Totowa, NJ

  • Print ISBN: 978-1-60761-160-8

  • Online ISBN: 978-1-60761-161-5

  • eBook Packages: MedicineMedicine (R0)

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