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The Neurological Manifestations of Sjögren’s Syndrome: Diagnosis and Treatment

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Sjögren’s Syndrome

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Abstract

This chapter addresses the following:

  1. (a)

    clinical neurological presentation,

  2. (b)

    laboratory investigation, and

  3. (c)

    treatment of peripheral and central nervous system diseases associated with Sjögren’s syndrome.

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Abbreviations

SS:

Sjögren’s syndrome

PNS:

Peripheral nervous system

CNS:

Central nervous system

ACL:

Anti-cardiolipin

APLS:

Anti-phospholipid antibodies syndrome

FMS:

Fibromyalgia syndrome

MGUS:

Monoclonal gammopathy of unknown significance

CIDP:

Chronic inflammatory demyelinating polyneuropathy

PML:

Progressive multifocal leukoencephalopathy

NMO:

Neuromyelitis optica (Devic’s syndrome)

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  1. Rheumatology Clinic, Scripps Memorial Hospital and Research Foundation, La Jolla, CA, USA

    Robert I. Fox

  2. Division of Rheumatology, The Jerome L. Greene Sjögren’s Syndrome Center, Johns Hopkins Bayview Medical Center, Baltimore, MD, USA

    Julius Birnbaum

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    Robert I. Fox

  2. Research Foundation, Rheumatology Clinic, Scripps Memorial Hospital &, Caminito Sinnecock 6565, La Jolla, 92037, California, USA

    Carla M. Fox

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Fox, R.I., Birnbaum, J. (2011). The Neurological Manifestations of Sjögren’s Syndrome: Diagnosis and Treatment. In: Fox, R., Fox, C. (eds) Sjögren’s Syndrome. Springer, New York, NY. https://doi.org/10.1007/978-1-60327-957-4_22

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