Abstract
The idiopathic interstitial pneumonias are a group of diffuse parenchymal lung diseases of unknown etiology with varying degrees of inflammation and fibrosis. They are classified into seven clinicopathological entities: idiopathic pulmonary fibrosis, nonspecific interstitial pneumonia, desquamative interstitial pneumonia, respiratory bronchiolitis/interstitial lung disease, organizing pneumonia, acute interstitial pneumonia, and lymphoid interstitial pneumonia. The diagnosis of the interstitial idiopathic pneumonias is clinical-radiological-pathological and requires the presence of an appropriate histological pattern in pulmonary biopsy. In idiopathic pulmonary fibrosis, a set of criteria has been established to permit diagnosis with a sensitivity of more than 90% when lung biopsy samples are not available. The only established treatment is based on glucocorticoids and immunossupressants, while lung transplantation is required in later stages.
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© 2008 Humana Press, a part of Springer Science+Business Media, LLC
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Xaubet, A., Molina-Molina, M., Serrano-Mollar, A. (2008). Idiopathic Interstitial Pneumonias. In: Shoenfeld, Y., Cervera, R., Gershwin, M.E. (eds) Diagnostic Criteria in Autoimmune Diseases. Humana Press. https://doi.org/10.1007/978-1-60327-285-8_71
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DOI: https://doi.org/10.1007/978-1-60327-285-8_71
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