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Abstract

Typical Cogan syndrome (CS) includes ocular involvement that is primarily interstitial keratitis (IK) with audiovestibular involvement such as sudden onset of nausea, vomiting, tinnitus, vertigo along with progressive hearing loss. The time interval between ocular and audiovestibular involvement may be as long as 2 years. A typical CS type includes patients with classic relapsing pattern of autoimmune-type vestibuloauditory symptoms in addition to the presentation of other types of inflammatory eye disease, with or without IK. Another group includes patients with more than 2 years between the onset of the ophthalmogic symptoms and the audiovestibular manifestations. A third group includes patients with typical ocular manifestations associated, within 2 years, with audiovestibular symptoms different from Meniere-like episodes.

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© 2008 Humana Press, a part of Springer Science+Business Media, LLC

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Kessel, A., Toubi, E. (2008). Cogan Syndrome. In: Shoenfeld, Y., Cervera, R., Gershwin, M.E. (eds) Diagnostic Criteria in Autoimmune Diseases. Humana Press. https://doi.org/10.1007/978-1-60327-285-8_25

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