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Huntington’s Disease

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Psychiatry for Neurologists

Part of the book series: Current Clinical Neurology ((CCNEU))

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Abstract

Huntington’s disease (HD) is an autosomal dominant, progressive, neurodegenerative disorder first described in detail by George Huntington in 1872. Symptoms of HD include an extrapyramidal motor disorder, cognitive impairment, and psychiatric syndromes. Impairments in all three domains may occur simultaneously in an individual patient, or separately over the course of the illness. Behavioral and cognitive changes may precede the onset of neurological signs. Because few psychiatrists have experience in caring for patients with HD, the neurologist often must be adept in evaluation and treatment of both neurological and behavioral abnormalities.

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Author information

Authors and Affiliations

  1. Departments of Psychiatry and Neurology, University of Maryland Hospital, University of Maryland School of Medicine, Baltimore, MD

    Karen E. Anderson MD

  2. Department of Neurology, Neurological Institute of New York, Columbia University College of Physicians and Surgeons, New York, NY

    Karen S. Marder MD, MPH

Authors
  1. Karen E. Anderson MD
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  2. Karen S. Marder MD, MPH
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Editor information

Editors and Affiliations

  1. Department of Psychiatry and Neurosciences, University of California, San Diego

    Dilip V. Jests MD

  2. Department of Psychiatry and Neurosciences, VA San Diego Healthcare System, San Diego, CA

    Dilip V. Jests MD

  3. Parkinson’s Disease and Movement Disorders Center, NeuroHealth, Warwick, RI

    Joseph H. Friedman MD

  4. University Medical School, Providence, RI

    Joseph H. Friedman MD

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© 2006 Humana Press Inc., Totowa, NJ

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Anderson, K.E., Marder, K.S. (2006). Huntington’s Disease. In: Jests, D.V., Friedman, J.H. (eds) Psychiatry for Neurologists. Current Clinical Neurology. Humana Press. https://doi.org/10.1007/978-1-59259-960-8_18

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  • DOI: https://doi.org/10.1007/978-1-59259-960-8_18

  • Publisher Name: Humana Press

  • Print ISBN: 978-1-58829-483-8

  • Online ISBN: 978-1-59259-960-8

  • eBook Packages: MedicineMedicine (R0)

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