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Nutrition and Bone Health pp 635–646Cite as

The Role of Nutrition for Bone Health in Cystic Fibrosis

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Abstract

Cystic fibrosis (CF) is a common genetic disorder in the United States, affecting approx 1 in 3200 white and 1 in 15,000 black live births (1). This disease results in abnormal sodium and chloride transport resulting from mutations in the CF transmembrane conductance regulator (CFTR) (2). Mutations in the CFTR alter the osmolarity of body secretions, resulting in lung and gastrointestinal (GI) complications. Blocked bronchial airways, lung infections, and GI disturbances involving maldigestion and malabsorption are common consequences of CF.

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Authors
  1. Kimberly O. O’Brien
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  2. Michael F. Holick
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Editors and Affiliations

  1. Department of Medicine, Dermatology, Physiology, and Biophysics, Boston University School of Medicine, Boston, MA, USA

    Michael F. Holick PhD, MD

  2. Human Nutrition Research Center on Aging, Tufts University, Boston, MA, USA

    Bess Dawson-Hughes MD

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O’Brien, K.O., Holick, M.F. (2004). The Role of Nutrition for Bone Health in Cystic Fibrosis. In: Holick, M.F., Dawson-Hughes, B. (eds) Nutrition and Bone Health. Nutrition and Health. Humana Press, Totowa, NJ. https://doi.org/10.1007/978-1-59259-740-6_34

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  • DOI: https://doi.org/10.1007/978-1-59259-740-6_34

  • Publisher Name: Humana Press, Totowa, NJ

  • Print ISBN: 978-1-61737-451-7

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