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Critical Care Neurology and Neurosurgery pp 541–552Cite as

Management of the Patient With Mitochondrial Disease in the Neurosciences Critical Care Unit

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Part of the book series: Current Clinical Neurology ((CCNEU))

Abstract

The term mitochondrial disorder (MD) encompasses a group of diseases that result from the structural, biochemical, or genetic derangement of mitochondria. In simple terms, MDs are disorders of deficient cellular energy production (1). The role of MD in aging and in a wide variety of systemic and neurologic disorders is increasingly recognized (2). Mitochondrial disorders may present as independent syndromes, complicate other medical disorders, or occur as complication of therapies used to treat other disorders (1). Most patients with MD are not diagnosed on initial presentation but present with recurrent episodic symptoms that elude diagnosis for months to years.

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Authors
  1. Julio A. Chalela
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Editors and Affiliations

  1. Neurosciences Critical Care, University Hospitals of Cleveland, Case Western Reserve University, Cleveland, OH, USA

    Jose I. Suarez MD

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© 2004 Springer Science+Business Media New York

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Chalela, J.A. (2004). Management of the Patient With Mitochondrial Disease in the Neurosciences Critical Care Unit. In: Suarez, J.I. (eds) Critical Care Neurology and Neurosurgery. Current Clinical Neurology. Humana Press, Totowa, NJ. https://doi.org/10.1007/978-1-59259-660-7_31

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  • DOI: https://doi.org/10.1007/978-1-59259-660-7_31

  • Publisher Name: Humana Press, Totowa, NJ

  • Print ISBN: 978-1-61737-350-3

  • Online ISBN: 978-1-59259-660-7

  • eBook Packages: Springer Book Archive

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