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Cutaneous Vascular Malformations

  • Chapter
Pathology of Vascular Skin Lesions

Part of the book series: Current Clinical Pathology ((CCPATH))

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Abstract

Malformation denotes an abnormal structure that results from an aberration in embryologic development. Although the term malformation is conventionally used as a synonym for hamartoma, the two are different, because hamartoma refers to a potpourri of tissue elements normally present at a particular site. Vascular malformations can be either functional or anatomic. In the case of functional abnormalities, the changes are related mostly to physiologic changes, as is the case for nevus anemicus. In contrast, anatomic vascular malformations exhibit evident morphologic abnormalities of the involved vessels. Anatomic vascular malformations are subdivided into the following groups: capillary, venous, arterial, lymphatic, and combined anomalies (Table 1). Clinically, it is important to separate the vascular malformations into those of low flow and high flow. Low-flow abnormalities include malformations of capillary, venous, lymphatic, or combination, whereas high-flow abnormalities include arteriovenous malformations (1).

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  1. Departments of Pathology and Dermatology, Wake Forest University School of Medicine, Winston-Salem, NC, USA

    Omar P. Sangüeza MD

  2. Department of Dermatology Fundación Jiménez Díaz, Universidad Autonoma, Madrid, Spain

    Luis Requena MD

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Sangüeza, O.P., Requena, L. (2003). Cutaneous Vascular Malformations. In: Pathology of Vascular Skin Lesions. Current Clinical Pathology. Humana Press, Totowa, NJ. https://doi.org/10.1007/978-1-59259-360-6_5

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  • DOI: https://doi.org/10.1007/978-1-59259-360-6_5

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