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Practical Management of Pediatric Ocular Disorders and Strabismus pp 291–296Cite as

Electroretinography in Pediatric Retinal Dystrophies

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Abstract

The use of full-field electroretinography (ERG) is crucial to the diagnosis and understanding of retinal dystrophies in pediatric patients. It is also important to elucidate the etiology of nystagmus in infants, ruling in or out the presence of a retinal etiology. Congenital retinal dystrophies can be categorized by their effect on rods or cones, and further by whether they are stationary or progressive. Here we describe the procedure of performing an ERG in the pediatric patient and use the aforementioned classification method to outline the characteristics of some of the retinal dystrophies, including the use of ERG in their diagnoses.

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Suggested Reading

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Acknowledgements

We would like to acknowledge Retinal Physician magazine, published by PentaVision LLC, for granting permission to use Fig. 28.1. The electrodiagnostic facilities are supported by the National Institute of Health Core grant 5P30EY019007, the NCI Core grant 5P30CA013696, and unrestricted funds from Research to Prevent Blindness, Columbia University, New York. S.H.T. is a member of the RD-CURE Consortium and is supported by the Tistou and Charlotte Kerstan Foundation, NIH R01EY018213, EY024698, the Research to Prevent Blindness Physician-Scientist Award, the Schneeweiss Stem Cell Fund, New York State (N09G-302 and N13G-275), the Foundation Fighting Blindness New York Regional Research Center Grant (C-NY05-0705-0312), Kobi and Nancy Karp, and the Gebroe Family Foundation.

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Authors and Affiliations

  1. Department of Ophthalmology, Columbia University, New York, NY, 10032, USA

    James Lin MD, Luz Amaro-Quireza OD & Stephen H. Tsang MD, PhD

  2. Barbara & Donald Jonas and Bernard & Shirlee Brown Electrodiagnostic Laboratory, Columbia University, New York, NY, 10032, USA

    Stephen H. Tsang MD, PhD

  3. Department of Pathology & Cell Biology, Columbia University, New York, NY, 10032, USA

    Stephen H. Tsang MD, PhD

  4. Institute of Human Nutrition, Columbia University, New York, NY, 10032, USA

    Stephen H. Tsang MD, PhD

  5. Herbert Irving Comprehensive Cancer Center, Columbia University, New York, NY, 10032, USA

    Stephen H. Tsang MD, PhD

Authors
  1. James Lin MD
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  2. Luz Amaro-Quireza OD
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  3. Stephen H. Tsang MD, PhD
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Corresponding author

Correspondence to Stephen H. Tsang MD, PhD .

Editor information

Editors and Affiliations

  1. Cole Eye Institute, Cleveland Clinic, Cleveland, Ohio, USA

    Elias Traboulsi

  2. Abrahamson Pediatric Eye Institute, Cincinnati Children's Hospital, Cincinnati, Ohio, USA

    Virginia Utz

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Lin, J., Amaro-Quireza, L., Tsang, S.H. (2016). Electroretinography in Pediatric Retinal Dystrophies. In: Traboulsi, E., Utz, V. (eds) Practical Management of Pediatric Ocular Disorders and Strabismus. Springer, New York, NY. https://doi.org/10.1007/978-1-4939-2745-6_28

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  • DOI: https://doi.org/10.1007/978-1-4939-2745-6_28

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  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4939-2744-9

  • Online ISBN: 978-1-4939-2745-6

  • eBook Packages: MedicineMedicine (R0)

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