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Persistence of the Fetal Vasculature: Varieties and Management

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Abstract

The spectrum of persistence of the fetal vasculature (PFV) is broad and includes anterior segment as well as vitreal and retinal abnormalities. The great majority of cases are unilateral and not associated with other systemic abnormalities. Some patients can be observed and the ocular abnormalities are inconsequential; others require surgical interventions such as lens extraction, anterior vitrectomy, and occasionally posterior vitreoretinal maneuvers. Rarely, patients have very small eyes with disorganized vitreous and a very poor visual outcome; in such cases, the lens is often removed to avoid angle closure glaucoma and phthisis bulbi. Accurate diagnosis and appropriate management are associated with acceptable outcomes in a majority of cases.

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Author information

Authors and Affiliations

  1. Cleveland Clinic Foundation, Cole Eye Institute, i-20, 9500 Euclid Avenue, Cleveland, OH, 44195, USA

    Priyanka Kumar MD

  2. Cleveland Clinic, Cole Eye Institute, i32, 9500 Euclid Avenue, Cleveland, OH, 44195, USA

    Elias I. Traboulsi MD, MEd

Authors
  1. Priyanka Kumar MD
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  2. Elias I. Traboulsi MD, MEd
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Corresponding author

Correspondence to Elias I. Traboulsi MD, MEd .

Editor information

Editors and Affiliations

  1. Cole Eye Institute, Cleveland Clinic, Cleveland, Ohio, USA

    Elias Traboulsi

  2. Abrahamson Pediatric Eye Institute, Cincinnati Children's Hospital, Cincinnati, Ohio, USA

    Virginia Utz

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Kumar, P., Traboulsi, E.I. (2016). Persistence of the Fetal Vasculature: Varieties and Management. In: Traboulsi, E., Utz, V. (eds) Practical Management of Pediatric Ocular Disorders and Strabismus. Springer, New York, NY. https://doi.org/10.1007/978-1-4939-2745-6_20

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  • DOI: https://doi.org/10.1007/978-1-4939-2745-6_20

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  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4939-2744-9

  • Online ISBN: 978-1-4939-2745-6

  • eBook Packages: MedicineMedicine (R0)

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