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Idiopathic Hypersomnia

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Sleep Medicine

Abstract

More than half a century ago, Prof. Roth recognized a leading symptom of idiopathic hypersomnia—sleep drunkenness—and described the first patients with prolonged nocturnal sleep accompanied by excessive daytime sleepiness with long unrefreshing naps and protracted and difficult awakening. The term idiopathic hypersomnia was given a variety of clinical labels including idiopathic central nervous hypersomnia or hypersomnolence, functional hypersomnia, mixed or harmonious hypersomnia, hypersomnia with automatic behavior, and nonrapid eye movement (REM) narcolepsy. Two different clinical forms recommended by Prof. Roth—polysymptomatic and monosymptomatic—disappeared for decades. Thanks to Prof. Billiard’s unflagging effort, two forms—idiopathic hypersomnia with long and without long sleep time—reappeared in the latest International Classification of Sleep Disorders, second edition (ICSD-2) classification. However, the biological background of these clinical entities remains unknown, and much effort is needed to shed more light on its pathophysiology.

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Author information

Authors and Affiliations

  1. Department of Neurology, 1st Faculty of Medicine, Charles University, Katerinska 30, 128 00, Prague 2, Czech Republic

    Prof Sona Nevsimalova MD, DSc

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  1. Prof Sona Nevsimalova MD, DSc
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Correspondence to Sona Nevsimalova MD, DSc .

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Editors and Affiliations

  1. Department of Neurology, New Jersey Neuroscience Institute JFK Medical Center, Edison, New Jersey, USA

    Sudhansu Chokroverty

  2. Department of Neurology, Gui de Chauliac Hospital, Montpellier, France

    Michel Billiard

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Nevsimalova, S. (2015). Idiopathic Hypersomnia. In: Chokroverty, S., Billiard, M. (eds) Sleep Medicine. Springer, New York, NY. https://doi.org/10.1007/978-1-4939-2089-1_27

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  • DOI: https://doi.org/10.1007/978-1-4939-2089-1_27

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  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4939-2088-4

  • Online ISBN: 978-1-4939-2089-1

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