Abstract
Dermatofibrosarcoma protuberans (DFSP), first described clinically by Darier and Ferrand in 1924 and histopathologically by Taylor and Helwig in 1962, represents a rare low-grade malignancy with a tendency for local recurrence and minimal capacity to produce distant metastasis. Its pathogenesis and histogenesis are not completely known. DFSP has been reported to arise at the site of previous radiotherapy or trauma, in burn scars, and in surgical and immunization sites. Over the years, different lines of differentiation for DFSP have been proposed: fibroblastic, histiocytic, and neural.
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Margaritescu, I., Chirita, A.D. (2015). Dermatofibrosarcoma Protuberans. In: Rare Malignant Skin Tumors. Springer, New York, NY. https://doi.org/10.1007/978-1-4939-2023-5_32
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DOI: https://doi.org/10.1007/978-1-4939-2023-5_32
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