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Gastrointestinal, Pancreatic and Hepatic Malignancies in Children

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Pediatric Malignancies: Pathology and Imaging

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Abstract

Gastroenteropancreatic neuroendocrine tumors account for 36 % of all neuroendocrine tumors in the pediatric age group. The most common site of occurrence is the appendix. Gastrointestinal stromal tumors are rare in children with the vast majority occurring in the stomach and in girls around the median age of 13 years. Pancreatic malignancy in childhood is distinctly rare, and this chapter discussion is restricted to solid pseudopapillary neoplasm, pancreatoblastoma, and pancreatic neuroendocrine tumors. The liver is the third most common site of origin for solid abdominal tumors in children, and this chapter discusses the more common malignant tumors hepatoblastoma, hepatocellular carcinoma, fibrolamellar hepatocellular carcinoma, and undifferentiated embryonal sarcoma.

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Authors and Affiliations

  1. Neil D. Johnson Chair of Radiology Informatics, Department of Radiology, Cincinnati Children’s Hospital Medical Center, 3333 Burnet Avenue, MLC 5031, Cincinnati, OH, 45229, USA

    Alexander J. Towbin M.D.

  2. UCSF Benioff Children’s Hospital Oakland, Oakland, CA, USA

    Jon M. Rowland M.D., Ph.D.

  3. Children’s Hospital Los Angeles, University of Southern California, Los Angeles, CA, USA

    David M. Parham M.D.

Authors
  1. Alexander J. Towbin M.D.
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  2. Jon M. Rowland M.D., Ph.D.
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  3. David M. Parham M.D.
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Correspondence to Alexander J. Towbin M.D. .

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Editors and Affiliations

  1. Department of Pathology and Laboratory Medicine, Children’s Hospital Los Angeles, University of Southern California, Los Angeles, California, USA

    David M. Parham

  2. Associate Professor of Pathology and Laboratory Medicine, The University of Texas M.D. Anderson Cancer Center, Houston, Texas, USA

    Joseph D. Khoury

  3. Department of Radiological Sciences, St. Jude Children's Research Hospital, Memphis, Tennessee, USA

    M. Beth McCarville

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Towbin, A.J., Rowland, J.M., Parham, D.M. (2015). Gastrointestinal, Pancreatic and Hepatic Malignancies in Children. In: Parham, D., Khoury, J., McCarville, M. (eds) Pediatric Malignancies: Pathology and Imaging. Springer, New York, NY. https://doi.org/10.1007/978-1-4939-1729-7_9

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  • DOI: https://doi.org/10.1007/978-1-4939-1729-7_9

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