Abstract
There are several hereditary syndromes associated with endocrine or neuroendocrine dysfunction. Examples such as von Hippel-Lindau syndrome and its association with pancreatic neuroendocrine tumors and pheochromocytomas and Carney complex and the associated endocrine hyperactivity belong to this broad category. This chapter will focus on the two most common syndromes related to endocrine hyperactivity and tumor formation, multiple endocrine neoplasia (MEN) types 1 and 2.
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Brewer, J.J. (2015). Multiple Endocrine Neoplasia (MEN) Syndromes. In: Chu, Q., Gibbs, J., Zibari, G. (eds) Surgical Oncology. Springer, New York, NY. https://doi.org/10.1007/978-1-4939-1423-4_25
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DOI: https://doi.org/10.1007/978-1-4939-1423-4_25
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