Abstract
The term ‘benign myopathies of childhood’ is used to describe a group of disorders sometimes referred to as congenital myopathies, although in some instances they may not cause symptoms until later in childhood or even until adult life. These disorders usually have a genetic basis, although this may not be apparent. In most patients weakness is mild or moderate, and marked wasting is unusual. These disorders are usually only slowly progressive and, in some, improvement may occur with increasing maturity (Dubowitz, 1978; 1980).
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© 1991 M. Swash and M.S. Schwartz
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Swash, M., Schwartz, M.S. (1991). ‘Benign’ myopathies of childhood. In: Biopsy Pathology of Muscle. Biopsy Pathology Series. Springer, Boston, MA. https://doi.org/10.1007/978-1-4899-3400-0_7
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DOI: https://doi.org/10.1007/978-1-4899-3400-0_7
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