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Vasculitis in primary Sjögren’s syndrome

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The Vasculitides

Abstract

Sjögren’s syndrome (SS) is a chronic autoimmune disease, characterized by lymphocytic infiltration of the exocrine glands resulting in xerostomia and keratoconjunctivitis sicca. These manifestations can occur al.one (primary SS) or in association with other autoimmune disorders, such as rheumatoid arthritis or systemic lupus erythematosus (secondary SS). Extraglandular manifestations are seen in approximately half of SS patients and include Raynaud’s phenomenon, splenomegaly, lymphad-enopathy, lung involvement, kidney involvement, liver involvement and vasculitis [1].

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Authors
  1. A. G. Tzioufas
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  2. F. N. Skopouli
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  3. D. Boumba
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  4. H. M. Moutsopoulos
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Editor information

Editors and Affiliations

  1. Division of Rheumatology, Clinical Research Centre, Northwick Park Hospital, London, UK

    B. M. Ansell (Consultant Rheumatologist and Former Head) (Consultant Rheumatologist and Former Head)

  2. Rheumatology Department, University of Birmingham, Birmingham, UK

    P. A. Bacon (Professor of Rheumatology and Head) (Professor of Rheumatology and Head)

  3. Division of Anatomic Pathology, University of California Davis School of Medicine, Sacramento, California, USA

    J. T. Lie (Professor and Director) (Professor and Director)

  4. University of California Davis Medical Center, Sacramento, California, USA

    J. T. Lie (Professor and Director) (Professor and Director)

  5. Division of Rheumatology, Department of Medicine, Cerrahpasa Medical Faculty, University of Istanbul, Turkey

    H. Yazici (Professor and Chief) (Professor and Chief)

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© 1996 Springer Science+Business Media Dordrecht

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Tzioufas, A.G., Skopouli, F.N., Boumba, D., Moutsopoulos, H.M. (1996). Vasculitis in primary Sjögren’s syndrome. In: Ansell, B.M., Bacon, P.A., Lie, J.T., Yazici, H. (eds) The Vasculitides. Springer, Boston, MA. https://doi.org/10.1007/978-1-4899-2889-4_19

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  • DOI: https://doi.org/10.1007/978-1-4899-2889-4_19

  • Publisher Name: Springer, Boston, MA

  • Print ISBN: 978-0-412-64140-4

  • Online ISBN: 978-1-4899-2889-4

  • eBook Packages: Springer Book Archive

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