Argininosuccinic Aciduria in Adult : A Clinical, Electrophysiological and Biochemical Study

  • T. Grisar
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 153)


Argininosuccinic aciduria is an hereditary disorder of the urea cycle in which argininosuccinase (As; EC: is defective or absent. The defect may be detected by the finding of the over-excretion of argininosuccinic acid (ASA) and of negligible levels of enzyme activity in erythrocyte lysates.


Uric Acid Serum Uric Acid Urea Cycle Contingent Negative Variation Theta Rhythm 
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Copyright information

© Springer Science+Business Media New York 1982

Authors and Affiliations

  • T. Grisar
    • 1
  1. 1.Institute of Medicine, Department of NeurologyUniversity of LiègeLiègeBelgium

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